In this case, the anaesthetic management of a child with limb-girdle muscular dystrophy is presented.
📌 3 Key Takeaways
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Objective & Hypothesis:Limb-girdle muscular dystrophies are a group of disorders with wide genetic and clinical heterogeneity.
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Key Findings & Data:These disorders may lead to an increase in life-threatening complications related to surgery and anaesthesia.
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Conclusion & Impact:In this case, the anaesthetic management of a child with limb-girdle muscular dystrophy is presented.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Limb-girdle muscular dystrophies are a group of disorders with wide genetic and clinical heterogeneity. These disorders may lead to an increase in life-threatening complications related to surgery and anaesthesia. In this case, the anaesthetic management of a child with limb-girdle muscular dystrophy is presented.
Özet
Limb-girdle müsküler distrofileri, genetik ve klinik özellikleri açısından farklılıklar gösteren bir hastalık grubudur. Bu hastalıklar cerrahi ve anestezi ile ilişkili yaşamı tehdit eden komplikasyonlara neden olabilir. Bu olguda limb-girdle müsküler distrofili bir çocuk hastanın anestezi uygulaması sunulmaktadır.
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Cite This Article
SARKILAR, G., MERMER, A., YÜCEKUL, M., ÇEKEN, B. M., ALTUN, C., OTELCİOĞLU, Ş. (2014). Anaesthetic management of a child with Limb-Girdle muscular dystrophy. Türk Anestezi ve Reanimasyon Dergisi, Cilt: 42 - Sayı: 2, 103–105. https://ajindex.com/articles/414118
Straub V, Bushby K. The chilhood limb-girdle muscular dystrophies. Semin Pediatr Neurol 2006; 13: 104-14. [CrossRef] Driessen JJ. Neuromuscular and mitochondrial disorders: what is relevant to the anaesthesiologist?. Curr Opin Anaesthesiol 2008; 21: 350-5. [CrossRef] Gurnaney H, Brown A, Litman RS. Malignant hyperthermia and muscular dystrophies. Anesth Analg 2009; 109: 1043-8. [CrossRef] Kocum A, Sener M, Calişkan E, Aribogan A. Anesthetic management for a child with unknown type of limb-girdle muscular dystrophy. Pediatr Int 2010; 52: 37-8. [CrossRef] Richa FC. Anaesthetic management of a patient with limb-girdle muscular dystrophy for laparoscopic cholecystectomy. Eur J Anaesthesiol 2011; 28: 72-3. [CrossRef] Fruen BR, Mickelson JR, Roqhair TJ, Litterer LA, Louis CF. Effects of propofol on Ca2+ regulation by malignant hyperthermia- susceptible muscle membranes. Anesthesiology 1995; 82: 1274-82. [CrossRef ] Xue FS, Liu KP, Liu Y, Xu YC, Liao X, Zhang GH, et al. Assessment of small-dose fentanyl and sufentanil blunting the cardiovascular responses to laryngoscopy and intubation in children. Paediatr Anaesth 2007; 17: 568-74. [CrossRef] de Boer HD, van Esmond J, Booij LH, Driessen JJ. Reversal of rocuronium- induced profound neuromuscular block by sugammadex in Duchenne muscular dystrophy. Paediatr Anaesth 2009; 19: 1226-8. [CrossRef] Hayes J, Veyckemans F, Bissonnette B. Duchenne muscular dystrophy: an old anesthesia problem revisited. Paediatr Anaesth 2008; 18: 100-6.