Journals / Türk Anestezi ve Reanimasyon Dergisi / 2005 / Cilt: 33 - Sayı: 2

Anaesthesia approach for von hippel-lindau syndrome with cerebellar hemangioblastoma and pheochromocytoma (Case report)

Von hippel-lindau sendromlu bir hastada serebellar hemangioblastoma ve feokromositoma ameliyatında anestezi yaklaşımı

Pages
181–185
Publication Date
2022-11-04
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Renal or pancreatic cysts, hypernephroma and pheochromacytoma are other associated findings.This case report reviews anaesthetic considerations for the patient with VHLS and presents the anaesthesia management of a patients with VHLS undergoing surgery for a cerebellar mass and intraabdominal pheochromocytoma.

📌 3 Key Takeaways

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Objective & Hypothesis:Von Hippel-Lindau Syndome (VHLS) is a rarely seen autosomal dominant disease characterized by retinal and central nervous system capillary hemangioblastomas.
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Key Findings & Data:Von Hippel-Lindau Syndome (VHLS) is a rarely seen autosomal dominant disease characterized by retinal and central nervous system capillary hemangioblastomas.
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Conclusion & Impact:Renal or pancreatic cysts, hypernephroma and pheochromacytoma are other associated findings.This case report reviews anaesthetic considerations for the patient with VHLS and presents the anaesthesia management of a patients with VHLS undergoing surgery for a cerebellar mass and intraabdominal pheochromocytoma.
🔬Design:Review & Systematic Survey
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Von Hippel-Lindau Syndome (VHLS) is a rarely seen autosomal dominant disease characterized by retinal and central nervous system capillary hemangioblastomas. Renal or pancreatic cysts, hypernephroma and pheochromacytoma are other associated findings.This case report reviews anaesthetic considerations for the patient with VHLS and presents the anaesthesia management of a patients with VHLS undergoing surgery for a cerebellar mass and intraabdominal pheochromocytoma.

Özet

Von Hippel-Lindau Sendromu (VHLS) retinanın veya santral sinir sisteminin kapiller hemangioblastomu ile karakterize, ender görülen otozomal dominant bir hastalıktır. Renal veya pankreatik kist, hipernefroma ve feokromositoma patolojiye eşlik edebilir.VHLS tanısı konan olguda serebellar kitle ve feokromositoma operasyonu için uygulanan anestezi yönetimi literatür eşliğinde sunulmuştur.

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Cite This Article

AKIN, Ş., TÜRKÖZ, A., BİLEN, A., ÖNER, S. Ö., TUNA, N. (2022). Anaesthesia approach for von hippel-lindau syndrome with cerebellar hemangioblastoma and pheochromocytoma (Case report). Türk Anestezi ve Reanimasyon Dergisi, Cilt: 33 - Sayı: 2, 181–185. https://ajindex.com/articles/620147

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References (6)

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