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Journals / Anadolu Tıp Dergisi / 2001 / Cilt: 3 - Sayı: 1

Degos' syndrome might have a benign course? Evaluation of two cases

Degos sendromu benign seyirli olabilir mi? İki olgunun incelenmesi

Tekinalp GELEN
Gülten KARPUZOĞLU
Gülsüm Özlem ELPEK
Erkan ALPSOY
Pages
37–40
Publication Date
2022-10-10
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

The clinicopathologic findings showed that, Degos' Syndrome might occur without systemic manifestations and survival for a longer period may be possible for the cases, in which the only presentation is skin involvement.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Degos' Syndrome is a rare systemic disorder characterized by typical skin lesions.
📊
Key Findings & Data:We report two cases, in which lymphocyte-mediated vasculitis throughout the dermis with necrosis of the vessel wall was the most consistent microscopic feature and any systemic manifestation could not been detected during the follow-up.
💡
Conclusion & Impact:The clinicopathologic findings showed that, Degos' Syndrome might occur without systemic manifestations and survival for a longer period may be possible for the cases, in which the only presentation is skin involvement.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Degos' Syndrome is a rare systemic disorder characterized by typical skin lesions. We report two cases, in which lymphocyte-mediated vasculitis throughout the dermis with necrosis of the vessel wall was the most consistent microscopic feature and any systemic manifestation could not been detected during the follow-up. The clinicopathologic findings showed that, Degos' Syndrome might occur without systemic manifestations and survival for a longer period may be possible for the cases, in which the only presentation is skin involvement.

Özet

Degos Sendromu tipik deri lezyonları ile karakterli ve nadir görülen bir sistemik hastalıktır. Bu yazıda takipleri boyunca sistemik bulgu saptanmayan, deri lezyonlarında histopatolojik olarak tüm deride damar duvarları boyunca nekrozun eşlik ettiği lenfositik vaskülitin baskın olduğu iki Degos Sendromu olgusu sunulmuştur. Klinikopatolojik bulgular Degos Sendromunun sistemik bulgu vermeksizin ortaya çıkabileceği ve sadece deri tutulumu ile seyrettiğinde hastaların yaşam süresinin daha uzun olabileceğini göstermektedir.

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Cite This Article

GELEN, T., KARPUZOĞLU, G., ELPEK, G. Ö., ALPSOY, E. (2022). Degos' syndrome might have a benign course? Evaluation of two cases. Anadolu Tıp Dergisi, Cilt: 3 - Sayı: 1, 37–40. https://ajindex.com/articles/438165

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