Journals / Tıp Araştırmaları Dergisi / 2012 / Cilt: 10 - Sayı: 3

Ohtahara Syndrome: A case report

Ohtahara sendromu: Bir olgu sunumu

Pages
106–108
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Patient was diagnosed with Ohtahara Syndrome due to electroencephalography findings.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Ohtahara Syndrome (early infantile epileptic encephalopathy) is the earliest developing syndrome among the age dependent epileptic encephalopathies.
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Key Findings & Data:A 10-day patient was admitted to our hospital with convulsion complaints which were resistant to anticonvulsants.
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Conclusion & Impact:Patient was diagnosed with Ohtahara Syndrome due to electroencephalography findings.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Ohtahara Syndrome (early infantile epileptic encephalopathy) is the earliest developing syndrome among the age dependent epileptic encephalopathies. It mostly develops in the first month and especially in the first ten days after birth. It is characterized with recurrent tonic spasms and suppression-burst pattern in the electroencephalography. A 10-day patient was admitted to our hospital with convulsion complaints which were resistant to anticonvulsants. Patient was diagnosed with Ohtahara Syndrome due to electroencephalography findings.

Özet

Ohtahara Sendromu (Erken infantil epileptic ensefalopati) yaşa bağımlı epileptik ensefalopatilerin en erken ortaya çıkanıdır. Genellikle yaşamın ilk ayında ve sıklıkla ilk on gününde ortaya çıkan, sık tekrarlayan tonik spazmlar ve elektroensefalografide supresyon-burst paterni ile karakterizedir. On günlükken konvulsiyon şikayetiyle getirilen antikonvülzanlara dirençli konvulsiyonları olan elektroensefalografide supresyon-burst paterni görülen hasta Ohtahara Sendromu tanısı aldı.

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Cite This Article

SAL, E., PEKER, E., DOĞAN, M., BAŞARANOĞLU, M., ÇAKSEN, H. (2012). Ohtahara Syndrome: A case report. Tıp Araştırmaları Dergisi, Cilt: 10 - Sayı: 3, 106–108. https://ajindex.com/articles/361715

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References (12)

  1. Ohtahara S. Clinico-electrical delineation of epileptic encephalopathies in childhood. Asian Med J 1978; 21:499–509.
  2. Aicardi J, Ohtahara S. Severe neonatal epilepsies with suppression-burst pattern. In: Roger J, Bureau M, Dravet Ch, Genton P, Tassinari CA, Wolf P, editors. Epileptic syndromes in infancy, childhood and adolescence. 4th ed. London: John Libbey Eurotext Ltd; 2005:39–50.
  3. Ohtahara S, Yamatogi Y, Ohtsuka Y. Early epileptic encephalopathies. In: Wallace SJ, Farrell K, editors. Epilepsy in children. London: Arnold; 2004; 133–141.
  4. Sabiha A. Çocuk nörolojisi, Alp ofset matbaacılık mak. sanayi ve ticaret ltd. şti. 2006: 70. Yamatogi Y, Ohtahara S. Early infantile epileptic encephalopathy with suppression- bursts. Ohtahara syndrome; it’s overview referring to our 16 cases. Brain Dev 2002; 24:13–23.
  5. Komaki H, Sugai K, Sasaki M, et al. Surgical treatment of a case of early infantile epileptic encephalopathy with suppression-bursts associated with focal cortical dysplasia. Epilepsia 1999; 40:365–369.
  6. Yiş U, Dirik E, Kurul S. Çocukluk Çağında Epileptik Ensefalopatiler. DEÜ tıp fakültesi dergisi 2006; 20 (3):183–191.
  7. Clarke M, Gill J, Noronha M, McKinley I. Early infantile epileptic encephalopathy with suppression burst: Ohtahara Syndrome. Dev Med Child Neurol 1987; 29:520–528. Taşdemir HA. Yenidoğan Dönemi Epileptik Sendromları. Güncel pediatri 1.Uludağ Pediatri Kış Kongresi özel sayısı 2005; 21–23.
  8. Schlumberger E, Dulac O, Plouin P. Early infantile syndrome with suppression-burst: nosological considerations: In: Roger J, Bureau M, Dravet C, Dreifuss FE, Perret A, Wolf P, editors. Epileptic syndromes of infancy, childhood and adolescence. 2nd ed. London: John Libbey, 1992; 35–42.
  9. Martin HJ, Deroubaix-Tella P, Thelliez PH. Encephalopathine Epileptique neonatale a bouffees periodiques: a brief over view. J Clin Neorophysiol 2003; 20(6):393–397.
  10. Yamatogi Y, Ohtahara S. Age-dependent epileptic encephalopathy: a longitudinal study. Folia Psychiatr Neurol Jpn 1981; 35(3):321– 332. Bermejo AM, Martin VL, Arcas J et al. Early infantile epileptic encephalopathy: a case associated with hemimegalencephaly. Brain Dev 1992; 14:425–428.
  11. Williams AN, Gray RG, Poulton K, Ramani P, Whitehouse WPA. A case of Ohtahara syndrome with cytocrom oxydase deficiency. Dev Med Child Neurol 1998; 40:568–570.
  12. Miller SP, Dilenge ME, Meagher-Villemure K, O’Gorman AM, Shevell MI. Infantile epileptic encephalopathy (Ohtahara Syndrome) and migrational disorder. Pediatr Neurol 1998; 19:50–5