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Journals / Astım Allerji İmmünoloji / 2015 / Cilt: 13 - Sayı: 2

Retrospective evaluation of patient with primary immunodefi ciency patients; Erzurum experience

Primer immün yetmezlik hastalarımızın Primer immün yetmezlik hastalarımızın retrospektif değerlendirilmesi; Erzurum deneyimi retrospektif değerlendirilmesi; Erzurum deneyimi

Demet HAFIZOĞLU
DİLARA FATMA KOCACIK UYGUN
Pages
90–93
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

So we think that the doctors, who care with pediatric population, should be educated for PID patients.

📌 3 Key Takeaways

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Objective & Hypothesis:Objective: Th e aim of study is to determine the clinical features of our patients with primary immunodefi ciency in a region of eastern Turkey.Materials and Methods: Th e medical records with primary immunodefi ciency (PID) who were followed ornewly diagnosed in Ataturk University School of Medicine and Erzurum Regional Training and Research Hospital Department of Pediatric Immunology and Allergy between June 2013 and June 2015 were evaluated retrospectively.Results: Totally 100 patients were followed in our center.
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Key Findings & Data:Antibody defi ciency was seen in 80% of patients while other immunodefi ciencies were phagocytic system defects in 6%, severe combined immunodefi ciency in 5%, immun disregulation defects in 4%, innate immun system defects in 2%, other defects in 3%.Discussion: Other than the patients living in Erzurum, the patients from the Eastern Anatolia Region are also usually admitting to Erzurum hospitals.
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Conclusion & Impact:So we think that the doctors, who care with pediatric population, should be educated for PID patients.
🔬Design:Research Article
📍Scope:2013 Verileri
⚙️Variables:Domain Parameters

Abstract

Objective: Th e aim of study is to determine the clinical features of our patients with primary immunodefi ciency in a region of eastern Turkey.Materials and Methods: Th e medical records with primary immunodefi ciency (PID) who were followed ornewly diagnosed in Ataturk University School of Medicine and Erzurum Regional Training and Research Hospital Department of Pediatric Immunology and Allergy between June 2013 and June 2015 were evaluated retrospectively.Results: Totally 100 patients were followed in our center. Antibody defi ciency was seen in 80% of patients while other immunodefi ciencies were phagocytic system defects in 6%, severe combined immunodefi ciency in 5%, immun disregulation defects in 4%, innate immun system defects in 2%, other defects in 3%.Discussion: Other than the patients living in Erzurum, the patients from the Eastern Anatolia Region are also usually admitting to Erzurum hospitals. Wethink that the PID patients in this region are more than our known patients. So we think that the doctors, who care with pediatric population, should be educated for PID patients.

Özet

Giriş: Bu çalışmanın amacı, Doğu Anadolu bölgesindeki primer immün yetmezlikli (PİY) olgularımızı değerlendirmek.Gereç ve Yöntem: Atatürk Üniversitesi Tıp Fakültesi ve Erzurum Bölge Eğitim Araştırma Hastanesi Çocuk İmmünoloji-Allerji bölümlerinde Haziran 2013-Haziran 2015 tarihleri arasında takip edilen ve yeni tanı alan PİY'li olgular retrospektif olarak değerlendirildi.Bulgular: Merkezimizde toplam 100 hasta izlemdeydi. Olguların %80'inde antikor eksiklikleri görülürken %6 olguda fagositer sistem defekti, %5 olguda ağır kombine immün yetmezlik, %4 olguda immün disregülasyon defektleri, %2 olguda doğal immün sitem defekti, %3 olguda diğer immün yetmezliklere rastlanmıştır.Sonuç: Erzurum Bölgesi'ne doğunun diğer illerinden de hasta sevki sıklıkla yapılmaktadır. Bu bölgede PİY'li daha fazla hasta olduğu kanaatindeyiz. Bu nedenle çocuk sağlığı ile uğraşan tüm sağlık personelinin bilinçlendirilmesi önem taşımaktadır.

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Cite This Article

HAFIZOĞLU, D., UYGUN, D. F. K. (2015). Retrospective evaluation of patient with primary immunodefi ciency patients; Erzurum experience. Astım Allerji İmmünoloji, Cilt: 13 - Sayı: 2, 90–93. https://ajindex.com/articles/149699

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