Journals / Türk Oftalmoloji Dergisi / 2021 / Cilt: 51 - Sayı: 6

Straatsma Syndrome: Should Visual Prognostic Factors Be Taken into Account? A Case Report

Straatsma Sendromu: Görme Keskinliği Prognostik Faktörleri Dikkate Alınmalı mı? Olgu Sunumu

Pages
398–402
Publication Date
2022-11-06
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Keywords: Amblyopia, myelinated retinal nerve fibers, straatsma syndrome, prognostic factors

📌 3 Key Takeaways

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Objective & Hypothesis:Straatsma syndrome is the triad of myelinated retinal nerve fibers, myopia, and amblyopia and may be associated with strabismus, nystagmus, hypoplastic optic nerve, and heterochromia iridum.
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Key Findings & Data:The degree of anisometropia, presence of strabismus, extent of myelination, and macular involvement have been reported to be associated with poor visual acuity after occlusion therapy for amblyopia in this syndrome.
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Conclusion & Impact:Keywords: Amblyopia, myelinated retinal nerve fibers, straatsma syndrome, prognostic factors
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Straatsma syndrome is the triad of myelinated retinal nerve fibers, myopia, and amblyopia and may be associated with strabismus, nystagmus, hypoplastic optic nerve, and heterochromia iridum. The degree of anisometropia, presence of strabismus, extent of myelination, and macular involvement have been reported to be associated with poor visual acuity after occlusion therapy for amblyopia in this syndrome. Here we present two cases of Straatsma syndrome with different responses to occlusion therapy and discuss their treatment responses according to prognostic factors for post-occlusion visual acuity. Keywords: Amblyopia, myelinated retinal nerve fibers, straatsma syndrome, prognostic factors

Özet

Straatsma sendromu, miyelinize retinal sinir lifi, miyopi ve ambliyopi triadından oluşmakta ve strabismus, nistagmus, hipoplastik optik sinir ve iris heterokromisi bu sendroma eşlik edebilmektedir. Anizometropinin derecesi, strabismusun varlığı, miyelinizasyonun genişliği, ve maküler tutulumun varlığı literatürde Straatsma sendromu olgularında ambliyopi için uygulanan kapama tedavisi sonrası görme keskinliği açısından kötü prognoz ile ilişkilendirilmiştir. Bu bildirinin amacı, kapama tedavisine farklı yanıtlar aldığımız iki Straatsma sendromu olgusunu sunmak ve tedavi yanıtlarını literatürde bildirilen kapama tedavisi sonrası görme keskinliğinin prognostik faktörlerine göre tartışmaktır. Anahtar Kelimeler: Ambliyopi, miyelinize retinal sinir lifi, straatsma sendromu, prognostik faktörler

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Cite This Article

ŞAHİN, Ö., SEVİK, M. O., AYKUT, A., KARAMAN, N. F. (2022). Straatsma Syndrome: Should Visual Prognostic Factors Be Taken into Account? A Case Report. Türk Oftalmoloji Dergisi, Cilt: 51 - Sayı: 6, 398–402. https://ajindex.com/articles/637588

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