Aritmojenik sağ ventrikül kardiyomiyopatisi bulunan tek yumurta ikizi kız kardeşler ve birinde ısrarcı sol üst vena kava sendromu ile komplike ICD implantasyonu
Arrhythmogenic right ventricular cardiomyopathy in monozygotic twin sisters, and persistent left superior vena cava in one complicating implantation of ICD
This report presents monozygotic twins withARVC, suggesting a genetic abnormality as the most prob- able cause.
📌 3 Key Takeaways
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Objective & Hypothesis:Arrhythmogenic right ventricular cardiomyopa- thy (ARVC) is an inherited cardiomyopathy characterizedhistologically by fibro-fatty replacement of heart muscle,and clinically by ventricular arrhythmias and right ventricu- lar dysfunction.
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Key Findings & Data:Arrhythmogenic right ventricular cardiomyopa- thy (ARVC) is an inherited cardiomyopathy characterizedhistologically by fibro-fatty replacement of heart muscle,and clinically by ventricular arrhythmias and right ventricu- lar dysfunction.
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Conclusion & Impact:This report presents monozygotic twins withARVC, suggesting a genetic abnormality as the most prob- able cause.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Arrhythmogenic right ventricular cardiomyopa- thy (ARVC) is an inherited cardiomyopathy characterizedhistologically by fibro-fatty replacement of heart muscle,and clinically by ventricular arrhythmias and right ventricu- lar dysfunction. This report presents monozygotic twins withARVC, suggesting a genetic abnormality as the most prob- able cause.
Özet
Aritmojenik sağ ventrikül kardiyomiyopatisi kalp kası- nın histolojik olarak fibroz-yağlı doku ile yer değiştirdiği veklinik olarak ventriküler aritmi ve sağ ventrikül fonksiyonubozukluğu ile karakterize kalıtsal bir kardiyomiyopatidir. Bu- rada biz aritmojenik sağ ventrikül kardiyomiyopatili tek yu- murta ikizlerini sunuyoruz; hastalığın en olası nedeni olarakgenetik anormallik gözükmektedir.
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Cite This Article
ASTARCIOĞLU, M. A., KİLİT, C., ŞEN, T., YAYMACI, M., AMASYALI, B. (2022). Aritmojenik sağ ventrikül kardiyomiyopatisi bulunan tek yumurta ikizi kız kardeşler ve birinde ısrarcı sol üst vena kava sendromu ile komplike ICD implantasyonu. Türk Kardiyoloji Derneği Arşivi, Cilt: 43 - Sayı: 7, 644–647. https://ajindex.com/articles/633526
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