Journals / Türk Kardiyoloji Derneği Arşivi / 2000 / Cilt: 28 - Sayı: 11

Cardiac amyloidosis involving the pericardium: A case report

Perikardiyal tutulum gösteren kardiyak amiloidoz: Olgu sunumu

Pages
701–702
Publication Date
2022-11-06
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Pericarditis with effusion is very rare and rarely results in tamponade in cardiac amyloidosis.In this report, a case with cardiac amyloidosis involving pericardium is presented and reviewed the cardiac amyloidosis.

📌 3 Key Takeaways

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Objective & Hypothesis:Amyloidosis results from the deposition of fibrous amyloid proteins, frequently in the extracellular spaces of tissues and organs.
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Key Findings & Data:In systemic amyloidosis, cardiac manifestations consist primarly of congestive heart failure and cardiomegaly and a variety of arrhythmias.
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Conclusion & Impact:Pericarditis with effusion is very rare and rarely results in tamponade in cardiac amyloidosis.In this report, a case with cardiac amyloidosis involving pericardium is presented and reviewed the cardiac amyloidosis.
🔬Design:Review & Systematic Survey
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Amyloidosis results from the deposition of fibrous amyloid proteins, frequently in the extracellular spaces of tissues and organs. In systemic amyloidosis, cardiac manifestations consist primarly of congestive heart failure and cardiomegaly and a variety of arrhythmias. These manifestations prominantly reflect diffuse involvement by myocardium amyloid, the endocardium, and valves. Pericarditis with effusion is very rare and rarely results in tamponade in cardiac amyloidosis.In this report, a case with cardiac amyloidosis involving pericardium is presented and reviewed the cardiac amyloidosis.

Özet

Amiloidoz, fibröz amiloid proteinlerin sıklıkla doku ve organların ekstraselüler boşluklarında birikmesi sonucu meydana gelen bir hastalıktır.Sistemik amiloidozda, kardiyak tutulumun bulguları kardiyomegali, konjestif kalp yetersizliği ve kardiyak aritmilerdir. Bu belirtiler özellikle endokardiyum ve kapakların diffüz amiloid tutulumunu yansıtmaktadır. Kardiyak amiloidozda efüzyonla birlikte seyreden perikardit çok nadir olup sıklıkla tamponada yol açmamaktadır. Bu makalede perikardiyal tutulum gösteren kardiyak amiloidoz olgusu sunularak kardiyak amiloidoz gözden geçirilmiştir.

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Cite This Article

AKDENİZ, B., GÖLDELİ, Ö., GÜNERİ, S. (2022). Cardiac amyloidosis involving the pericardium: A case report. Türk Kardiyoloji Derneği Arşivi, Cilt: 28 - Sayı: 11, 701–702. https://ajindex.com/articles/634113

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