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Journals / Türkderm-Deri Hastalıkları ve Frengi Arşivi / 2010 / Cilt: 44 - Sayı: 1

Bullous pemphigoid: A rare childhood disease with eleveted immunoglobulin E levels

Büllöz pemfigoid: Artmış immünglobulin E ile seyreden nadir bir çocukluk çağı hastalığı

Hayrullah ALP
Melike KESER
Hatice TOY
Pages
35–37
Publication Date
2022-11-05
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Also, this is the youngest case of bullous pemphigoid that is not associated with the maternal pemphigoid gestationis.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Bullous pemphigoid is a rare pemphigoid disease characterized by separation at the dermal-epidermal junction and common blisters clinically.
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Key Findings & Data:We have presented a 4 month-old case who developed tense bullae during her first month of life and diagnosed as bullous pemphigoid with elevated serum IgE levels.
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Conclusion & Impact:Also, this is the youngest case of bullous pemphigoid that is not associated with the maternal pemphigoid gestationis.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Bullous pemphigoid is a rare pemphigoid disease characterized by separation at the dermal-epidermal junction and common blisters clinically. We have presented a 4 month-old case who developed tense bullae during her first month of life and diagnosed as bullous pemphigoid with elevated serum IgE levels. In spite of the elevated serum IgE levels, the patient received benefit from the topical steroid treatment. Also, this is the youngest case of bullous pemphigoid that is not associated with the maternal pemphigoid gestationis.

Özet

Büllöz pemfigoid, nadir görülen bir pemfigoid grubu hastalık olup dermal-epidermal bileşkede ayrılma ve klinik olarak yaygın büller ile karakterizedir. Makalemizde, hayatının ilk ayında gergin büller gelişen ve artmış serum IgE seviyesi bulunan 4 aylık bir olguyu sunduk. Yüksek serum IgE seviyesine rağmen olgumuz verilen topikal steroid tedavisinden fayda gördü. Olgu, literatürdeki gebelik pemfigoidine bağlı olmayan en genç hasta özelliğini de taşımaktadır.

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Cite This Article

ALP, H., KESER, M., TOY, H. (2022). Bullous pemphigoid: A rare childhood disease with eleveted immunoglobulin E levels. Türkderm-Deri Hastalıkları ve Frengi Arşivi, Cilt: 44 - Sayı: 1, 35–37. https://ajindex.com/articles/622043

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