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Journals / Türk Anestezi ve Reanimasyon Dergisi / 2010 / Cilt: 38 - Sayı: 5

Anesthetic management in A pediatric patient with metachromatic leukodystrophy

Metakromatik lökodistrofili pediyatrik bir hastada anestezi yönetimi

Ayşegül CEYHAN
Özgün CUVAŞ
Solmaz ERUYAR
Pages
383–387
Publication Date
2022-11-05
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Here we aimed to report our anesthetic management of a pediatric patient with metachromatic leukodystrophy.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Metachromatic leukodystrophy is a progressive demyelinating neurological disorder caused by deficient activity of the enzyme arylsulphatase A.
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Key Findings & Data:In patients with metachromatic leukodystrophy, general anesthetic management should be carefully implemented in consideration of the potential risk of aspiration and airway complications due to poor pharyngeal muscle control and oral secretions.
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Conclusion & Impact:Here we aimed to report our anesthetic management of a pediatric patient with metachromatic leukodystrophy.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Metachromatic leukodystrophy is a progressive demyelinating neurological disorder caused by deficient activity of the enzyme arylsulphatase A. In patients with metachromatic leukodystrophy, general anesthetic management should be carefully implemented in consideration of the potential risk of aspiration and airway complications due to poor pharyngeal muscle control and oral secretions. Here we aimed to report our anesthetic management of a pediatric patient with metachromatic leukodystrophy.

Özet

Metakromatik lökodistrofi, arilsülfataz A enziminin yetersiz aktivitesinin neden olduğu ilerleyici demiyelinizan bir nörolojik hastalıktır. Metakromatik lökodistrofili hastalarda, potansiyel aspirasyon riski, zayıf faringeal kas kontrolü ve oral sekresyonlara bağlı hava yolu komplikasyonları nedeniyle, genel anestezi uygulaması dikkatli bir şekilde yürütülmelidir. Bu sunuda metakromatik lökodistrofili pediyatrik bir hastaya olan anestezik yaklaşımımızı sunmayı amaçladık.

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Cite This Article

CEYHAN, A., CUVAŞ, Ö., ERUYAR, S. (2022). Anesthetic management in A pediatric patient with metachromatic leukodystrophy. Türk Anestezi ve Reanimasyon Dergisi, Cilt: 38 - Sayı: 5, 383–387. https://ajindex.com/articles/619908

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References (8)

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