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Journals / Türk Anestezi ve Reanimasyon Dergisi / 2013 / Cilt: 41 - Sayı: 4

The anaesthetic management of temporal tumour resection in a patient with type 1 glutaric aciduria

Tip-1 glutarik asidürisi olan temporal tümör rezeksiyonu uygulanan bir hastada anestezi deneyimimiz

Tuğhan UTKU
Yusuf TUNALI
Ayşe Çiğdem TÜTÜNCÜ
Fatiş ALTINDAŞ
Fatma AKÇIL EREN
Özlem DİLMEN KORKMAZ
Ercüment YENTÜR
Emre ERBABACAN
Pages
139–141
Publication Date
2022-11-05
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We report the anaesthetic management of temporatumour resection that lasted for 8 hours in a 16-year-old patient with GA- 1, and discuss the risks of malignant hyperthermia and propofol infusion syndrome.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Glutaric aciduria type 1 (GA-1) is an uncommon cerebral organic aci- duria.
📊
Key Findings & Data:Few cases with GA-1 who underwent general anaesthesia have been reported pre- viously, and there are no data on long-term anaesthetic management of patients with GA-1.
💡
Conclusion & Impact:We report the anaesthetic management of temporatumour resection that lasted for 8 hours in a 16-year-old patient with GA- 1, and discuss the risks of malignant hyperthermia and propofol infusion syndrome.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Glutaric aciduria type 1 (GA-1) is an uncommon cerebral organic aci- duria. The risk of acute encephalopathic crises and metabolic acidosis may present during anaesthetic and surgical or postsurgical periods. Few cases with GA-1 who underwent general anaesthesia have been reported pre- viously, and there are no data on long-term anaesthetic management of patients with GA-1. We report the anaesthetic management of temporatumour resection that lasted for 8 hours in a 16-year-old patient with GA- 1, and discuss the risks of malignant hyperthermia and propofol infusion syndrome.

Özet

Tip-1 glutarik asidüri nadir görülen bir organik serebral asidüridir. Anes- tezi ve cerrahi sırasında ya da cerrahi sonrası dönemde akut ensefalopatik kriz ve metabolik asidoz gelişebilir. Literatürde genel anestezi uygulanan tip-1 glutarik asidüri olguları çok az sayıda olup, uzun süreli anestezi uy- gulanan tip-1 glutarik asidüri olgusuna rastlamadık. Bu yazıda sekiz saat süreyle temporal tümor rezeksiyonu uygulanan 16 yaşında tip-1 glutarik asidürili bir hastada anestezi yönetimimizi ve malign hipertermi ve propo- fol infüzyon sendromu gelişme risklerini tartıştık.

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Cite This Article

UTKU, T., TUNALI, Y., TÜTÜNCÜ, A. Ç., ALTINDAŞ, F., EREN, F. A., KORKMAZ, Ö. D., YENTÜR, E., ERBABACAN, E. (2022). The anaesthetic management of temporal tumour resection in a patient with type 1 glutaric aciduria. Türk Anestezi ve Reanimasyon Dergisi, Cilt: 41 - Sayı: 4, 139–141. https://ajindex.com/articles/619727

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