Here, we present the case of a 16-year-old female patient who sufferedfrom recurrent life-threatening hemoptysis episodes due to right lower lobe pulmonaryartery aneurysms and was finally treated with pulmonary resection.
📌 3 Key Takeaways
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Objective & Hypothesis:Hughes–Stovin syndrome is an extremely rare autoimmune clinical disorder that is characterized by deep vein thrombosis with multiple pulmonary and/or bronchial arterial aneurysms.This syndrome is an important cardiovascular status that may manifest Behçet’s disease withsystemic aneurysms.
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Key Findings & Data:Hughes–Stovin syndrome is an extremely rare autoimmune clinical disorder that is characterized by deep vein thrombosis with multiple pulmonary and/or bronchial arterial aneurysms.This syndrome is an important cardiovascular status that may manifest Behçet’s disease withsystemic aneurysms.
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Conclusion & Impact:Here, we present the case of a 16-year-old female patient who sufferedfrom recurrent life-threatening hemoptysis episodes due to right lower lobe pulmonaryartery aneurysms and was finally treated with pulmonary resection.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Hughes–Stovin syndrome is an extremely rare autoimmune clinical disorder that is characterized by deep vein thrombosis with multiple pulmonary and/or bronchial arterial aneurysms.This syndrome is an important cardiovascular status that may manifest Behçet’s disease withsystemic aneurysms. Here, we present the case of a 16-year-old female patient who sufferedfrom recurrent life-threatening hemoptysis episodes due to right lower lobe pulmonaryartery aneurysms and was finally treated with pulmonary resection.
Özet
Hughes-Stovin sendromu, çok sayıda pulmoner ve/veya bronşiyal arter anevrizması bulunan derin ven trombozu ile kendini gösteren son derece nadir bir otoimmün klinik hastalıktır. Bu sendrom, Behçet hastalığını sistemik anevrizmalarla gösterebilen önemli bir kardiyovasküler durumdur. Bu yazıda, sağ alt lob pulmoner arter anevrizmaları nedeniyle tekrarlayan hayatı tehdit eden hemoptizi atakları olan ve son olarak pulmoner rezeksiyon ile tedavi edilen 16 yaşında bir kadın olguyu sunuyoruz.
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Cite This Article
DERDİYOK, O., EVMAN, S., YILMAZ, H., BAYSUNGUR, V. (2022). An Extraordinary Cause in the Etiology of Recurrent Massive Hemoptysis: Hughes–Stovin Syndrome. Southern Clinics of Istanbul Eurasia, Cilt: 30 - Sayı: 2, 181–183. https://ajindex.com/articles/592839
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