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Journals / Retina-Vitreus / 2019 / Cilt: 28 - Sayı: 2

Coexistence of Retinis Pigmentosa and Posterior Staphyloma: Case Series

Retinitis Pigmentosa ve Posterior Stefi lom Birlikteliği: Olgu Serisi

Bayram GÜLPAMUK
Kemal TEKİN
Hasan KIZILTOPRAK
Mehmet Yasin TEKE
Pages
198–203
Publication Date
2022-10-17
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

As the surgicaloutcomes are not always satisfactory, vitreous surgery should be undertaken after careful consideration of the potential risks and benefi ts forsuch macular abnormalities.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:We aimed to report a case series of coexistence of retinitis pigmentosa (RP) and posterior staphyloma (PS) and to describe their clinicaloutcomes.
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Key Findings & Data:All patients had myopic refraction and decreased visualacuity.
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Conclusion & Impact:As the surgicaloutcomes are not always satisfactory, vitreous surgery should be undertaken after careful consideration of the potential risks and benefi ts forsuch macular abnormalities.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

We aimed to report a case series of coexistence of retinitis pigmentosa (RP) and posterior staphyloma (PS) and to describe their clinicaloutcomes. This case series include three patients’ complete ophthalmological examinations including optical coherence tomography (OCT),fundus autofl orescence, fundus fl uorescein angiography and enhanced depth OCT. All patients had myopic refraction and decreased visualacuity. Dilated fundus examination revealed waxy pallor optic atrophy, arterial attenuation, mid-peripheral bone spicule pigmentations, andlarge posterior staphyloma. Additionally, macular pseudohole (MPH) and cystoid macular edema (CME) were also detected. Coexistence ofRP and PS is a rare condition that may result in serious visual complications. RP can also be accompanied by MPH and CME. As the surgicaloutcomes are not always satisfactory, vitreous surgery should be undertaken after careful consideration of the potential risks and benefi ts forsuch macular abnormalities.

Özet

Bu makalemizde, retinitis pigmentosa (RP) ve posterior stafi lom (PS) birlikteliğini içeren bir vaka serisini sunmayı ve bunların klinik sonuçlarını tanımlamayı amaçladık. Bu vaka serisi, üç hastanın optik koherens tomografi (OCT), fundus otofl oresansı, fundus fl öresein anjiyografi ve EDİOCT’yi içeren tam oftalmolojik muayenelerini içermektedir. Tüm hastalarda miyopik refraksiyon ile görme keskinliğinde azalma mevcuttu. Dilate fundus muayenesinde balmumu optik atrofi , arteriyel atenüasyon, midperiferal kemik spikülü pigmentasyonlar ve büyük posterior stafi lom saptandı. Ek olarak, maküler psödohole (MPH) ve kistoid maküler ödem (KMÖ) de tespit edildi. RP ve PS’nin varlığı ciddi görsel komplikasyonlarla sonuçlanabilen nadir bir durumdur. MPH ve KMÖ de eşlik edebilir. Cerrahi sonuçlar her zaman tatmin edici olmadığından, bu tip maküler anormallikler için vitreus cerrahisi dikkatle düşünülmelidir.

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Cite This Article

GÜLPAMUK, B., TEKİN, K., KIZILTOPRAK, H., TEKE, M. Y. (2022). Coexistence of Retinis Pigmentosa and Posterior Staphyloma: Case Series. Retina-Vitreus, Cilt: 28 - Sayı: 2, 198–203. https://ajindex.com/articles/589096

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