The patient demonstrated good performance overtime after the implantation including open set speech understanding and telephone use.
📌 3 Key Takeaways
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Objective & Hypothesis:Usher's Syndrome is an autosomal recessive disorder characterized by congenital hearing loss and retinitis pigmentosa.
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Key Findings & Data:Usher's Syndrome patients with severe to profound sensorineural hearing loss can be considered as candidates for cochlear implantation.
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Conclusion & Impact:The patient demonstrated good performance overtime after the implantation including open set speech understanding and telephone use.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Usher's Syndrome is an autosomal recessive disorder characterized by congenital hearing loss and retinitis pigmentosa. Usher's Syndrome patients with severe to profound sensorineural hearing loss can be considered as candidates for cochlear implantation. This case study reports a deaf-blind with Usher's Syndrome who received a cochlear implant, the audiological evaluation is presented and the therapy sessions are discussed. The patient demonstrated good performance overtime after the implantation including open set speech understanding and telephone use.
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Cite This Article
DERİNSU, U., CİPRUT, A. (2022). Cochlear implantation in a patient with Usher's syndrome. Marmara Medical Journal, Cilt: 15 - Sayı: 4, 258–261. https://ajindex.com/articles/578434
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Hinderink JB, Brokx JPL, Mens LH, Van Den Broek P. Results from four cochlear implant patients with Usher's Syndrome. Ann Otol Rhinol Laryngol 1994
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