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Journals / Anadolu Tıp Dergisi / 2001 / Cilt: 3 - Sayı: 1

Epidermolysis bullosa: A report of two cases and review of the literature

Epidermolizis Bülloza: 2 olgu sunumu ve literatürün gözden geçirilmesi

Önder TAN
Mehmet BEKERECİOĞLU
Bekir ATİK
Mustafa TERCAN
Pages
30–33
Publication Date
2022-10-10
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We aim at the review the epidermolysis bullosa with the treatment difficulties.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Epidermolysis bullosa is a rare, genetically determined, characterized by cutaneous blistering after minor trauma and scarring of the skin and mucous membranes.
📊
Key Findings & Data:The hands are particularly vulnerable because of the contact and shearing forces of normal daily activity.
💡
Conclusion & Impact:We aim at the review the epidermolysis bullosa with the treatment difficulties.
🔬Design:Review & Systematic Survey
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Epidermolysis bullosa is a rare, genetically determined, characterized by cutaneous blistering after minor trauma and scarring of the skin and mucous membranes. The hands are particularly vulnerable because of the contact and shearing forces of normal daily activity. The typical deformity is progressive encasement of the digits in a cocoon of atrophic scar. We aim at the review the epidermolysis bullosa with the treatment difficulties.

Özet

Deride ve mukozada travma sonrası bül oluşumu ve skar ile iyileşmesi ile karakterize, herediter nadir bir hastalıktır. Özellikle el parmaklarında deri füzyonu oluşarak, eller tipik olarak "koza" görünümü alır. Ellerdeki bu yapışıklıkların tedavisi, tekrarlaması nedeniyle güçtür. Biz, biri 10 diğeri 19 yaşında iki adet erkek epidermolizis bülloza olgusunu, tedavideki güçlükleri vurgulayarak, literatürün yeniden gözden geçirilmesini ve sunmayı amaçladık.

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Cite This Article

TAN, Ö., BEKERECİOĞLU, M., ATİK, B., TERCAN, M. (2022). Epidermolysis bullosa: A report of two cases and review of the literature. Anadolu Tıp Dergisi, Cilt: 3 - Sayı: 1, 30–33. https://ajindex.com/articles/438177

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