This article presents anesthetic management of CdLS syndrome suggesting difficult tracheal intubation on preoperative physical examination and evaluation of the anesthesiologic aspects of this syndrome.
📌 3 Key Takeaways
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Objective & Hypothesis:Cornelia de Lange (CdLS) is a rare dysmorphogenie syndrome characterized by distinctive facial appearence, failure to thrive and mental retardation.
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Key Findings & Data:Cornelia de Lange (CdLS) is a rare dysmorphogenie syndrome characterized by distinctive facial appearence, failure to thrive and mental retardation.
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Conclusion & Impact:This article presents anesthetic management of CdLS syndrome suggesting difficult tracheal intubation on preoperative physical examination and evaluation of the anesthesiologic aspects of this syndrome.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Çocuk · Kadın · De Lange sendromu
Abstract
Cornelia de Lange (CdLS) is a rare dysmorphogenie syndrome characterized by distinctive facial appearence, failure to thrive and mental retardation. This article presents anesthetic management of CdLS syndrome suggesting difficult tracheal intubation on preoperative physical examination and evaluation of the anesthesiologic aspects of this syndrome.
Özet
Cornelia de Lange sendromu (CdLS) nadir görülen, tipik yüz görünümü, büyüme geriliği ve mental retardasyonla karakterize bir sendromdur. Bu yazıda preoperatif değerlendirmede zor entübasyon olabileceği öngörülen bir CdLS olgusunun anestezi uygulaması ve bu olgulara anesteziyolojik yaklaşımların incelenmesi amaçlandı.
ÇEVİK, B., ÇOLAKOĞLU, S., AÇIKGÖZ, A., KİTAPÇI, İ. (2008). Cornelia de Lange syndrome and anesthesia (case report). Zeynep Kamil Tıp Bülteni, Cilt: 39 - Sayı: 2, 93–94. https://ajindex.com/articles/335596
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