We present a case of polymyositis with coexistence EB in this article.
📌 3 Key Takeaways
🎯
Objective & Hypothesis:Polymyositis, characterized with proximal muscle weakness, elevated serum muscle enzymes, myopathic findings on electromyography and muscle biopsy, is an inlammatory myopathy.
📊
Key Findings & Data:Epidermolysis bullosa (EB) is a rare disease which is characterized with bullae formation.
💡
Conclusion & Impact:We present a case of polymyositis with coexistence EB in this article.
Polymyositis, characterized with proximal muscle weakness, elevated serum muscle enzymes, myopathic findings on electromyography and muscle biopsy, is an inlammatory myopathy. Epidermolysis bullosa (EB) is a rare disease which is characterized with bullae formation. We present a case of polymyositis with coexistence EB in this article.
Özet
Polimiyozit, proksimal kas güçsüzlüğü, kas enzimlerinde yükseklik, elektromiyografide ve kas biyopsisinde miyopatik değişiklikler ile karakterize, inflamatuvar bir miyopatidir. Epidermolizis bulloza (EB) ise, bül oluşumuyla karakterize nadir bir hastalıktır. Burada, polimiyozit ile EB'nın birlikte görüldüğü bir olgu sunulmuştur.
Wojnarowska F, Eady RAJ, Burge SM. Bullous eruptions, congenital and inherited disorders. Champion RH, Burton JL, Burns DA, Breathnach SM, eds. Textbook of Dermatology. 6lh ed. Vol 3, 1998;1817-45
Shimizu H, Takizavva Y, Pulkkinen L, Murata S, et al. Epidermolysis bullosa simplex associated with muscular dystrophy: Phenotype-genotype correlations and review of the literatüre. J Am Acad Dermatol 1999;41:950-6
Mc Henry PM, Dagg JH, Tidman MJ, Lever RS. Epidermolysis bullosa acquisita occuring in association with systemic lupus erythematosus. Clin Exp Dermatol, 1993; 18:378-80
Ishikavva O, Warita S, Ohnishi K, Miyachi Y. A scleroderma-like variant of recessive dystrophic epidermolysis bullosa ? Br J Dermatol 1993; 129:602-5.