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Journals / Çocuk Dergisi / 2006 / Cilt: 6 - Sayı: 3

Hemitruncus: A rare congenital heart defect

Hemitrunkus: Ender bir doğumsal kalp hastalığı

Kemal NİŞLİ
Aygün DİNDAR
Şeref OLGAR
Naci ÖNER
Eker Rukiye ÖMEROĞLU
Türkan ERTUĞRUL
Atıf AKÇEVİN
Pages
216–218
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Early diagnosis surgical correction of this rare congenital heart defect is mandatory.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Ascending aortic origin of a branch of pulmonary artery is also named as hemitruncus arteriosus (HA).
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Key Findings & Data:It is a very rare congenital heart defect.
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Conclusion & Impact:Early diagnosis surgical correction of this rare congenital heart defect is mandatory.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Hipertansiyon · Kalp kusuru · doğuştan

Abstract

Ascending aortic origin of a branch of pulmonary artery is also named as hemitruncus arteriosus (HA). It is a very rare congenital heart defect. We report a case with HA whose right pulmonary artery was arising from the ascending aorta. The diagnosis was made by echocardiography at the age of one month. In addition the patient had patent ductus arteriosus, patent foramen ovale and right aortic arcus. The diagnosis of HA was confirmed by cardiac catheterization. Early diagnosis surgical correction of this rare congenital heart defect is mandatory.

Özet

Pulmoner arter dallarından birinin çıkan aortadan kaynaklanması hemitrunkus arteriozus (HA) olarak adlandırılır. Bu doğumsal kalp hastalığı çok ender olarak görülür. Bu yazıda sağ pulmoner arteri çıkan aortadan kaynak alan ve bir aylıkken ekokardiyografi ile tanı konan bir HA vakası sunulmuştur. Vakada, hemiturunkus ile beraber patent duktus arteriozus, patent foramen ovale ve sağ arkus aorta da tespit edilmiş. HA tanısı kardiyak kateterizasyon ile doğrulanmıştır. Bu ender doğumsal kalp hastalığında erken tanı ve cerrahi düzeltme zorunluluğu vurgulanmıştır.

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Cite This Article

NİŞLİ, K., DİNDAR, A., OLGAR, Ş., ÖNER, N., ÖMEROĞLU, E. R., ERTUĞRUL, T., AKÇEVİN, A. (2006). Hemitruncus: A rare congenital heart defect. Çocuk Dergisi, Cilt: 6 - Sayı: 3, 216–218. https://ajindex.com/articles/214083

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