Journals / Göğüs Kalp Damar Anestezi ve Yoğun Bakım Derneği Dergisi / 2016 / Cilt: 22 - Sayı: 3

Anaesthetic Management of A Patient with SturgeWeber Syndrome; Different Approach to Airway Management

Anestezi Yönetimi, Hava Yolu Yönetiminde Farklı Sturge-Weber Sendromlu Pediyatrik Hastada Bir Yaklaşım

Pages
128–130
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case, anesthesia management was presented in za pediatric patient with SWS scheduled for eye surgery with the diagnosis of glaucoma.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Sturge-Weber Syndrome (SWS) is a rare syndrome characterized by congenital skin angiomas and ensefalotrigeminal angiomatosis resulting in development of lesions on skin, brain and eyes.
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Key Findings & Data:Since patients with SWS have frequently angiomas in their airways, laryngoscopy, intubation, and ventilation by facemask should be performed very carefully Alternative airway devices should be ready for difficult airway management.
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Conclusion & Impact:In this case, anesthesia management was presented in za pediatric patient with SWS scheduled for eye surgery with the diagnosis of glaucoma.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Sturge-Weber Syndrome (SWS) is a rare syndrome characterized by congenital skin angiomas and ensefalotrigeminal angiomatosis resulting in development of lesions on skin, brain and eyes. Since patients with SWS have frequently angiomas in their airways, laryngoscopy, intubation, and ventilation by facemask should be performed very carefully Alternative airway devices should be ready for difficult airway management. In this case, anesthesia management was presented in za pediatric patient with SWS scheduled for eye surgery with the diagnosis of glaucoma.

Özet

Sturge-Weber Sendromu (SWS); deri, beyin ve göz ile ilgili lezyonlarla sonuçlanan, ensefalotrigeminal anjiomatozis ve konjenital deri anjiomları ile karakterize ender görülen bir sendromdur. SWS'li hastaların hava yollarında sıkça anjiomlar görülmesinden dolayı maske ile ventilasyonda, laringoskopi ve entübasyonda çok dikkatli olunmalıdır. Zor hava yolu yönetimi için alternatif hava yolu gereçleri hazır bulundurulmalıdır. Bu olguda, glokom nedeniyle göz cerrahisi planlanan SWS'li pediatrik hastada anestezi yönetimi sunuldu

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Cite This Article

AKBAŞ, S., ÖZKAN, A. S., POLAT, N., KADIOĞLU, M., DURMUŞ, M. (2016). Anaesthetic Management of A Patient with SturgeWeber Syndrome; Different Approach to Airway Management. Göğüs Kalp Damar Anestezi ve Yoğun Bakım Derneği Dergisi, Cilt: 22 - Sayı: 3, 128–130. https://ajindex.com/articles/178131

References (5)

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