Von Hippel Lindau Syndrome with Renal Cell Carcinoma, Pancreas Serous Cystadenoma, Hemangioblastoma and NET Demonstrated on Ga-68 DOTATATE PET-CT and FDG PET-CT Imaging
We hereby, report the rare case of a Von Hippel Lindau Syndrome with renal cell carcinoma, pancreas cystadenoma, hemangioblastoma and pancreatic NET demonstrated on both Ga-68 PSMA and FDG PET-CT imaging.
📌 3 Key Takeaways
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Objective & Hypothesis:Von Hippel–Lindau disease (VHL), also known as Von Hippel–Lindau syndrome, is a rare genetic disorder with multisystem involvement (1).
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Key Findings & Data:In recent years, much attention has been focused on 68Ga-PSMA PET-CT.
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Conclusion & Impact:We hereby, report the rare case of a Von Hippel Lindau Syndrome with renal cell carcinoma, pancreas cystadenoma, hemangioblastoma and pancreatic NET demonstrated on both Ga-68 PSMA and FDG PET-CT imaging.
🔬Design:Image Presentation
📍Scope:Comprehensive Sample
⚙️Variables:68 Ga PSMA PET-CT · FDG PET-CT · Von Hippel Lindau Syndrome
Abstract
Von Hippel–Lindau disease (VHL), also known as Von Hippel–Lindau syndrome, is a rare genetic disorder with multisystem involvement (1). Imaging plays an important role in the evaluation of cancer patients. In recent years, much attention has been focused on 68Ga-PSMA PET-CT. We hereby, report the rare case of a Von Hippel Lindau Syndrome with renal cell carcinoma, pancreas cystadenoma, hemangioblastoma and pancreatic NET demonstrated on both Ga-68 PSMA and FDG PET-CT imaging.
Özcan, P. P., Koç, Z. P., Yavan, G., Dirlik, M. M. (2022). Von Hippel Lindau Syndrome with Renal Cell Carcinoma, Pancreas Serous Cystadenoma, Hemangioblastoma and NET Demonstrated on Ga-68 DOTATATE PET-CT and FDG PET-CT Imaging. Molecular Oncologic Imaging, Volume: 2 Issue: 1. https://ajindex.com/articles/1626566
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