Budd-chiari syndrome in a young patient with celiac sprue: A case report

Temel Bulgular & Veri:Budd-Chiari sendromu ve çölyak spru birlikteliği nadirdir. 24 Yaşında bayan hasta, kliniğimize dört aydır süregelen güçsüzlük, karın şişliği ve kilo kaybı yakınmaları ile başvurdu.

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Sonuç & Katkı:Budd-Chiari ve malabsorpsiyon durumlarında çölyak spru akla getirilmelidir

🔬Tür:Araştırma Makalesi

📍Kapsam:Genişletilmiş Akademik Örneklem

⚙️Değişkenler:Çölyak hastalığı · Erişkin · Kadın

Özet

Budd-Chiari sendromu hepatik venlerin trombozudur ve çeşitli durumlarla birlikte olabilir. Budd-Chiari sendromu ve çölyak spru birlikteliği nadirdir. 24 Yaşında bayan hasta, kliniğimize dört aydır süregelen güçsüzlük, karın şişliği ve kilo kaybı yakınmaları ile başvurdu. Tetkikler sonucu Budd-Chiari sendromu ve malabsorpsiyon saptandı. Endomisyal antikorlar pozitifti ve intestinal villöz atrofi mevcuttu. Budd-Chiari etiyolojisinde bilinen nedenlerin araştırılması sonuçsuz kaldı. Glutensiz diyete alınan ve replasman tedavisi başlanan hasta, üç ay sonra umbilikal herni rüptürü ve bunu takiben gelişen asit infeksiyoınu ve renal yetmezlik tablosu ile kaybedildi. Budd-Chiari ve malabsorpsiyon durumlarında çölyak spru akla getirilmelidir

Abstract

Budd-Chiari syndrome is thrombosis of the hepatic veins, and associated conditions vary. Budd-Chiari and celiac sprue association is a rare condition. A 24-year-old woman was admitted to the clinic with complaints of weakness, distended abdomen and weight loss for four months. Results of investigation showed Budd-Chiari syndrome and malabsorption with endomysial antibodies and intestinal villous atrophy. All known etiological factors for Budd-Chiari syndrome were negative. Three months after initiation of a gluten-free diet and replacement therapy, she died from infection of ascitic fluid and renal failure following umbilical hernia rupture. Celiac sprue must be remembered especially in the event of Budd-Chiari syndrome and malabsorption

Anahtar kelimeler

Çölyak hastalığı Erişkin Kadın Hepatik ven trombozu Ölümle sonuçlanma Celiac Disease Adult Female Hepatic Vein Thrombosis Fatal Outcome

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Bu Makaleye Atıf Yap

DANALIOĞLU, A., POTUROĞLU, Ş., GÜLLÜOĞLU, G. M., DEMİR, K., BEŞIŞIK, F., ÇAKALOĞLU, Y., ÇEVİKBAŞ, U., ÖKTEN, A. (2003). Budd-chiari syndrome in a young patient with celiac sprue: A case report. Turkish Journal of Gastroenterology, Cilt: 14 - Sayı: 4, 262–265. https://ajindex.com/articles/411210

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Kaynakça (16)

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