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Journals / Turkish Journal of Gastroenterology / 2003 / Cilt: 14 - Sayı: 4

Genç bir hastada Budd-chiari sendromu ve çölyak spru birlikteliği: Olgu sunumu

Budd-chiari syndrome in a young patient with celiac sprue: A case report

Ahmet DANALIOĞLU
ŞULE POTUROĞLU
Güngör Mine GÜLLÜOĞLU
Kadir DEMİR
Fatih BEŞIŞIK
Yılmaz ÇAKALOĞLU
Uğur ÇEVİKBAŞ
Atilla ÖKTEN
Pages
262–265
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Celiac sprue must be remembered especially in the event of Budd-Chiari syndrome and malabsorption

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Budd-Chiari syndrome is thrombosis of the hepatic veins, and associated conditions vary.
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Key Findings & Data:A 24-year-old woman was admitted to the clinic with complaints of weakness, distended abdomen and weight loss for four months.
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Conclusion & Impact:Celiac sprue must be remembered especially in the event of Budd-Chiari syndrome and malabsorption
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Çölyak hastalığı · Erişkin · Kadın

Abstract

Budd-Chiari syndrome is thrombosis of the hepatic veins, and associated conditions vary. Budd-Chiari and celiac sprue association is a rare condition. A 24-year-old woman was admitted to the clinic with complaints of weakness, distended abdomen and weight loss for four months. Results of investigation showed Budd-Chiari syndrome and malabsorption with endomysial antibodies and intestinal villous atrophy. All known etiological factors for Budd-Chiari syndrome were negative. Three months after initiation of a gluten-free diet and replacement therapy, she died from infection of ascitic fluid and renal failure following umbilical hernia rupture. Celiac sprue must be remembered especially in the event of Budd-Chiari syndrome and malabsorption

Özet

Budd-Chiari sendromu hepatik venlerin trombozudur ve çeşitli durumlarla birlikte olabilir. Budd-Chiari sendromu ve çölyak spru birlikteliği nadirdir. 24 Yaşında bayan hasta, kliniğimize dört aydır süregelen güçsüzlük, karın şişliği ve kilo kaybı yakınmaları ile başvurdu. Tetkikler sonucu Budd-Chiari sendromu ve malabsorpsiyon saptandı. Endomisyal antikorlar pozitifti ve intestinal villöz atrofi mevcuttu. Budd-Chiari etiyolojisinde bilinen nedenlerin araştırılması sonuçsuz kaldı. Glutensiz diyete alınan ve replasman tedavisi başlanan hasta, üç ay sonra umbilikal herni rüptürü ve bunu takiben gelişen asit infeksiyoınu ve renal yetmezlik tablosu ile kaybedildi. Budd-Chiari ve malabsorpsiyon durumlarında çölyak spru akla getirilmelidir

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Cite This Article

DANALIOĞLU, A., POTUROĞLU, Ş., GÜLLÜOĞLU, G. M., DEMİR, K., BEŞIŞIK, F., ÇAKALOĞLU, Y., ÇEVİKBAŞ, U., ÖKTEN, A. (2003). Genç bir hastada Budd-chiari sendromu ve çölyak spru birlikteliği: Olgu sunumu. Turkish Journal of Gastroenterology, Cilt: 14 - Sayı: 4, 262–265. https://ajindex.com/articles/411210

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