Dergiler / Turkish Journal of Gastroenterology / 2017 / Cilt: 28 - Sayı: 5

Giant pancreatic solid cystic desmoid tumor with two ectopic adrenal tissues

Sayfa
401–404
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

We report the case for its rarity and huge size and to emphasize a regular follow-up because the long-term prognosis is currently unknown.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:A 19-year-old woman presented with painless swelling of the abdomen.
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Temel Bulgular & Veri:During surgery, a giant mass measuring 37 cm×26 cm×12 cm within the distal pancreas invading the spleen was noted.
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Sonuç & Katkı:We report the case for its rarity and huge size and to emphasize a regular follow-up because the long-term prognosis is currently unknown.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Özet

A 19-year-old woman presented with painless swelling of the abdomen. During surgery, a giant mass measuring 37 cm×26 cm×12 cm within the distal pancreas invading the spleen was noted. The clinical diagnosis of a solid cystic pseudopapillary tumor of the pancreas was suspected. Distal pancreatectomy, splenectomy, and debulking surgery were performed. Histological examination showed that the tumor infiltrated the spleen and pancreatic parenchyma, and sections of the solid areas revealed a proliferation of spindle-shaped or stellate cells growing in fascicular and storiform patterns within a myxoid intercellular matrix. Cystic areas were representing the entrapped excretory pancreatic ductules. Interestingly, there were two ectopic adrenal tissues found incidentally in the peripheral portion of the tumor. The histopathologic and immunohistochemical features were consistent with a solid cystic desmoid tumor of the pancreas. Desmoid tumors of the pancreas are very rare, and if they present as a solid cystic lesion, their diagnosis may be difficult. We report the case for its rarity and huge size and to emphasize a regular follow-up because the long-term prognosis is currently unknown.

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Bu Makaleye Atıf Yap

EKİNCİ, N., DİRİLENOĞLU, F., AVCI, A., ÖZŞAY, O. (2017). Giant pancreatic solid cystic desmoid tumor with two ectopic adrenal tissues. Turkish Journal of Gastroenterology, Cilt: 28 - Sayı: 5, 401–404. https://ajindex.com/articles/410179

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Kaynakça (14)

  1. Polistina F, Costantin G, D'Amore E, Ambrosino G. Sporadic, nontrauma-related, desmoid tumor of the pancreas: a rare diseasecase report and literature review. Case Rep Med 2010; 2010: 272760
  2. Amiot A, Dokmak S, Sauvanet A, et al. Sporadic desmoid tumor. An exceptional cause of cystic pancreatic lesion. JOP 2008; 9: 339- 45
  3. Clark SK, Phillips RKS. Desmoids in familial adenomatous polyposis. Br J Surg 1996; 83: 1494-504
  4. Tsukamotoa Y, Imakita M, Nishitani A, Ito T, Izukurac M, Hirotaa S. Pancreatic desmoid-type fibromatosis with beta-catenin gene mutation-Report of a case and review of the literature. Pathol Res Pract 2016; 212: 484-9
  5. Patel HD, Desai NR, Som A, Shah SK, Thosani NC. Solid-cystic pancreatic tail desmoid tumor with beta-catenin positivity. ACG Case Rep J 2017; 4: e40
  6. Lazar AJ, Hajibashi S, Lev D. Desmoid tumor: from surgical extirpation to molecular dissection. Curr Opin Oncol 2009; 21: 352-9
  7. Roggli VL, Kim HS, Hawkins E. Congenital generalized fibromatosis with visceral involvement. A case report. Cancer 1980; 45: 954-60
  8. Bhattacharya B, Dilworth HP, Iacobuzio-Donahue C, et al. Nuclear beta-catenin expression distinguishes deep fibromatosis from other benign and malignant fibroblastic and myofibroblastic lesions. Am J Surg Pathol 2005; 29: 653-9
  9. Lips DJ, Barker N, Clevers H, Hennipman A. The role of APC and beta-catenin in the aetiology of aggressive fibromatosis (desmoid tumors). Eur J Surg Oncol 2009; 35: 3-10
  10. Ballo MT, Zagars GK, Pollack A, Pisters PW, Pollack RA. Desmoid tumor: prognostic factors and outcome after surgery, radiation therapy, or combined surgery and radiation therapy. J Clin Oncol 1999; 17: 158-67
  11. Tanaka K, Yoshikawa R, Yanagi H, et al. Regression of sporadic intra-abdominal desmoid tumour following administration of nonsteroidal anti-inflammatory drug. World J Surg Oncol 2008; 6: 17
  12. Shimada S, Ishizawa T, Ishizawa K, Matsumura T, Hasegawa T, Hirose T. The value of MDM2 and CDK4 amplification levels using real-time polymerase chain reaction for the differential diagnosis of liposarcomas and their histologic mimickers. Hum Pathol 2006; 37: 1123-9
  13. Miettinen M, Lasota J. Gastrointestinal stromal tumors: review on morphology, molecular pathology, prognosis, and differential diagnosis. Arch Pathol Lab Med 2006; 130: 1466-78
  14. Xu B, Zhu LH, Wu JG, Wang XF, Matro E, Ni JJ. Pancreatic solid cystic desmoid tumor: case report and literature review. World J Gastroenterol. 2013; 19