Dergiler / Turkish Neurosurgery / 2013 / Cilt: 23 - Sayı: 1

Primary ewings sarcoma of cavernous sinus in an infant: A case report and review of literature

Bir infantta kavernöz sinüsün primer ewing sarkomu: Bir olgu sunumu ve literatürün gözden geçirilmesi

Sayfa
98–103
DOI
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Yapay Zeka Hızlı Bakış & Çıkarımlar

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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

The histological differential diagnosis of primary intracranial Ewing’s sarcoma / pPNET are discussed.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:Ewing’s / peripheral primitive neuroectodermal tumor (pPNET) of the cavernous sinus are extremely uncommon.
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Temel Bulgular & Veri:We present clinical,radiological, pathological findings of Ewing’s / pPNET involving the cavernous sinus in an eleven-month-old infant presenting with proptosisand 6th nerve palsy.
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Sonuç & Katkı:The histological differential diagnosis of primary intracranial Ewing’s sarcoma / pPNET are discussed.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Özet

Ewing’s / peripheral primitive neuroectodermal tumor (pPNET) of the cavernous sinus are extremely uncommon. We present clinical,radiological, pathological findings of Ewing’s / pPNET involving the cavernous sinus in an eleven-month-old infant presenting with proptosisand 6th nerve palsy. MRI Contrast scans showed a well-defined, homogenously enhancing mass involving the right cavernous sinus location.Histopathology and immunohistochemical features were consistent with Ewing’s/pPNET. The patient succumbed to disease in spite of startingchemotherapy. The clinical, radiological and pathological findings of previously reported cases of Ewing’s sarcoma / pPNET involving thecavernous sinus are summarized. The histological differential diagnosis of primary intracranial Ewing’s sarcoma / pPNET are discussed.

Abstract

Kavernöz sinüs Ewing / periferal primitif nöroektodermal tümörü (pPNET) son derece nadirdir. Proptosis ve 6. sinir palsisi ile gelen 11 aylık bir infantta kavernöz sinüsü tutan Ewing/pPNET klinik, radyolojik ve patolojik bulgularını sunuyoruz. Kontrastlı MRG taramaları sağ kavernöz sinüs konumunda iyi tanımlanmış, homojen olarak kontrast tutan bir kitle göstermiştir. Histopatoloji ve immünohistokimyasal özellikler Ewing/ pPNET ile tutarlı bulunmuştur. Kemoterapi başlanmasına rağmen hastamız hastalığı nedeniyle ölmüştür. Daha önceden bildirilen kavernöz sinüs Ewing sarkomu / pPNET vakalarının klinik, radyolojik ve patolojik bulguları özetlenmektedir. Primer intrakraniyal Ewing sarkomu / pPNET histolojik ayırıcı tanısı anlatılmıştır.

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Bu Makaleye Atıf Yap

PATIBANDLA, M. R., UPPIN, S. G., THOTAKURA, A. K., PANIGRAHI, M. K., CHALLA, S. (2013). Primary ewings sarcoma of cavernous sinus in an infant: A case report and review of literature. Turkish Neurosurgery, Cilt: 23 - Sayı: 1, 98–103. https://ajindex.com/articles/405479

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Kaynakça (1)

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