Prolonged QT with Multiple-Causation and its Succesful Multistage Therapy

Objective & Hypothesis:Prolonged QT (PQT) is a myocardial repolarization disorder characterized by a prolongation of the QT and a propensity to tachyarrhythmias, which may lead to torsades de pointes ventricular tachycardia (TdPVT), polymorphic ventricular tachycardia (PVT), and ventricular fibrillation.

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Key Findings & Data:There are two forms of the disorder, including congenital and acquired PQT.

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Conclusion & Impact:We report the current succesful therapies consisting of atrial pacing, lidocaine, and mexiletine for a PQT patient.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Uzamış QT · atriyal uyarma · meksiletin

Abstract

Prolonged QT (PQT) is a myocardial repolarization disorder characterized by a prolongation of the QT and a propensity to tachyarrhythmias, which may lead to torsades de pointes ventricular tachycardia (TdPVT), polymorphic ventricular tachycardia (PVT), and ventricular fibrillation. There are two forms of the disorder, including congenital and acquired PQT. There are many drugs and electrolyte disturbances that may lead to acquired form of PQT. Treatment of these two types of PQT at acute statement is similar. We report the current succesful therapies consisting of atrial pacing, lidocaine, and mexiletine for a PQT patient.

Özet

Uzamış QT (UQT), bir miyokardiyal repolarizasyon bozukluğu olup QT aralığının uzaması ve taşiaritmilerle karakterizedir. Bu durum; torsades depointes ventriküler taşikardisi (TdPVT), polimorfik ventriküler taşikardi (PVT) ve ventriküler fibrilasyona neden olabilir. Konjenital ve edinsel olmak üzere iki formu mevcuttur. Bu hastalığın edinsel formuna birçok ilaç veya elektrolit dengesizliği sebep olabilir. Edinsel ve konjenital formlarının akut dönemde tedavileri benzerdir. Biz olgu sunumumuzda tedaviye dirençli bir UQT hastasına yapılan; atriyal uyarma, lidokain ve meksiletin gibi güncel tedavi yöntemlerinin başarılı bir şekilde uygulanışını aktarmaya çalıştık.

Keywords

Uzamış QT atriyal uyarma meksiletin amiodaron Prolonged QT atrial pacing mexiletine amiodarone

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Cite This Article

KESKİN, M., ALPER, A. T., TÜRKKAN, C., TEKKEŞİN, A. İ. (2017). Prolonged QT with Multiple-Causation and its Succesful Multistage Therapy. Koşuyolu Heart Journal, Cilt: 20 - Sayı: 3, 265–268. https://ajindex.com/articles/90998

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