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Journals / Türk Nöroloji Dergisi / 2016 / Cilt: 22 - Sayı: 4

Ailesel Basınca Duyarlılık Nöropatisi Hastalığının Tuzak Nöropatili Hastalarda Elektrofizyolojik Tanı Sıklığı

The Neurophysiologic Frequency of Hereditary Neuropathy with Liability to Pressure Palsy in Entrapment Neuropathies

F. Göçmen YILDIZ
Sevim ÖZDAMAR ERDEM
Çağrı Mesut TEMUÇİN
Gülay NURLU
Pages
177–180
Publication Date
2022-11-05
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Results: Ten patients were diagnosed as having HNPP according to their genetic or nerve biopsy results; eight (80%) had bilateral Carpal tunnel syndrome, nine (90%) had bilateral ulnar entrapment neuropathy, eight (80%) had bilateral median and ulnar entrapment together; and three (30%) had one-sided peroneal neuropathy.Conclusion: Our data suggest that analyzing the neurophysiologic studies and keeping HNPP in mind are essential to characterize underdiagnosed patients with HNPP referred for entrapment neuropathy.

📌 3 Key Takeaways

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Objective & Hypothesis:Objective: Hereditary neuropathy with liability to pressure palsy (HNPP) needs to be differentiated from entrapment neuropathies due to differences in the treatment management.Materials and Methods: Among 5075 patients with entrapment neuropathy, we retrospectively evaluated the neurophysiologic results of 20 patients with three or more entrapments.
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Key Findings & Data:Objective: Hereditary neuropathy with liability to pressure palsy (HNPP) needs to be differentiated from entrapment neuropathies due to differences in the treatment management.Materials and Methods: Among 5075 patients with entrapment neuropathy, we retrospectively evaluated the neurophysiologic results of 20 patients with three or more entrapments.
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Conclusion & Impact:Results: Ten patients were diagnosed as having HNPP according to their genetic or nerve biopsy results; eight (80%) had bilateral Carpal tunnel syndrome, nine (90%) had bilateral ulnar entrapment neuropathy, eight (80%) had bilateral median and ulnar entrapment together; and three (30%) had one-sided peroneal neuropathy.Conclusion: Our data suggest that analyzing the neurophysiologic studies and keeping HNPP in mind are essential to characterize underdiagnosed patients with HNPP referred for entrapment neuropathy.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Objective: Hereditary neuropathy with liability to pressure palsy (HNPP) needs to be differentiated from entrapment neuropathies due to differences in the treatment management.Materials and Methods: Among 5075 patients with entrapment neuropathy, we retrospectively evaluated the neurophysiologic results of 20 patients with three or more entrapments. Results: Ten patients were diagnosed as having HNPP according to their genetic or nerve biopsy results; eight (80%) had bilateral Carpal tunnel syndrome, nine (90%) had bilateral ulnar entrapment neuropathy, eight (80%) had bilateral median and ulnar entrapment together; and three (30%) had one-sided peroneal neuropathy.Conclusion: Our data suggest that analyzing the neurophysiologic studies and keeping HNPP in mind are essential to characterize underdiagnosed patients with HNPP referred for entrapment neuropathy.

Özet

Amaç: Ailesel basınca duyarlılık nöropatisi (ABDN) tanısı diğer tuzak nöropatilerden tedavi yaklaşımlarındaki farklılıkları açısından ayrılmalıdır. Gereç ve Yöntem: 5075 elektrofizyolojik olarak tuzak nöropatisi tanısı konulan hastalar arasından, üç ve üçün üzerinde çoklu tuzak nöropatisi olan 20 hastanın elektrofizyolojik bilgileri geriye dönük olarak incelendi. Bulgular: Bu hastalar arasından on hastaya genetik veya biyopsi sonucuna göre ABDN tanısı konuldu. Tanı konulan sekiz (%80) hastada bilateral Karpal tünel sendromu, sekiz hastada (%80) bilateral ulnar sinir tuzaklanması, dokuz (%90) hastada hem bilateral medyan, hem de bilateral ulnar sinir tuzaklanması birlikte bulunmaktaydı. Üç (%30) ise tek taraflı peroneal sinir tuzaklanması bulunmaktaydı. Sonuç: Sonuçlarımız nörofizyolojik çalışma analizinin ve ABDN tanısının akılda tutulmasının nörofizyolojik olarak ABDN hastalarını, tuzaklanma nöropatisi için danışılan hastalardan ayrılmasına yardımcı olduğunu göstermektedir.

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Cite This Article

YILDIZ, F. G., ERDEM, S. Ö., TEMUÇİN, Ç. M., NURLU, G. (2022). Ailesel Basınca Duyarlılık Nöropatisi Hastalığının Tuzak Nöropatili Hastalarda Elektrofizyolojik Tanı Sıklığı. Türk Nöroloji Dergisi, Cilt: 22 - Sayı: 4, 177–180. https://ajindex.com/articles/636922

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