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Journals / Türk Kardiyoloji Derneği Arşivi / 2019 / Cilt: 47 - Sayı: 6

Left ventricular non-compaction in a patient with Shone’s complex

Shone anomalisi olan hastada sol ventriküler nonkompaksiyon

Leili POURAFKARI
Mehrnoush TOUFAN
Nader D NADER
Aidin Baghbani OSKOUEI
Pages
503–506
Publication Date
2022-11-05
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

To our knowledge, an association between NCC and Shone’s com- plex has not been previously described.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Shone’s complex is a rare congenital cardiac malformation characterized by serial obstructive lesions of the left heart at multiple levels.
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Key Findings & Data:Presently described is an unusual case of an adult male patient who presented with palpitations and worsening dyspnea.
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Conclusion & Impact:To our knowledge, an association between NCC and Shone’s com- plex has not been previously described.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Shone’s complex is a rare congenital cardiac malformation characterized by serial obstructive lesions of the left heart at multiple levels. Presently described is an unusual case of an adult male patient who presented with palpitations and worsening dyspnea. An echocardiographic evaluation revealed Shone’s complex associated with left ventricular non-compaction cardiomyopathy (NCC). To our knowledge, an association between NCC and Shone’s com- plex has not been previously described.

Özet

Shone kompleksi sol kalpte birçok düzeyde bir dizi obstrüktif lezyonla karakterize seyrek görülen bir doğuştan kardiyak malformasyondur. Burada çarpıntı ve artan nefes darlığı olan bir erişkin erkek hastaya ait olağandışı bir olgu sunuyoruz. Ekokardiyografik değerlendirme sol ventriküler nonkompaksiyon kardiyomiyopatiyle ilişkili Shone komplek- si lehineydi. Bildiğimiz kadarıyla bu kompleksle nonkom- paksiyon kardiyomiyopatinin ilişkisi daha önce tanımlanma- mıştı.

🔖

Cite This Article

POURAFKARI, L., TOUFAN, M., NADER, N. D., OSKOUEI, A. B. (2022). Left ventricular non-compaction in a patient with Shone’s complex. Türk Kardiyoloji Derneği Arşivi, Cilt: 47 - Sayı: 6, 503–506. https://ajindex.com/articles/632071

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