Journals / Journal of Neurological Sciences (Turkish) / 2015 / Cilt: 32 - Sayı: 3

Klippel-Feil Sendromunda C5 Spinöz Proçesinin Dev Hipertrofisi

A giant hypertrophy of C5 spinous process in Klippel-Feil syndrome

Pages
575–579
Publication Date
2022-10-19
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

To the best of our knowledge, thiscoexistence of congenital cervical bony anomalies in a child has not been reported previouslyin English literature.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Congenital cervical spinal anomalies are relatively common and can be seen in upper andlower cervical regions.
📊
Key Findings & Data:Here we reported an 11-year-old girl with unilateral hypertrophy ofthe lamina and spinous process of C5 vertebra coexistence with Klippel-Feil syndrome,occipitalization of atlas and atlantoaxial congenital fusion.
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Conclusion & Impact:To the best of our knowledge, thiscoexistence of congenital cervical bony anomalies in a child has not been reported previouslyin English literature.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Congenital cervical spinal anomalies are relatively common and can be seen in upper andlower cervical regions. However, hypertrophy of the lamina and spinous process of cervicalvertebra is extremely rare. Here we reported an 11-year-old girl with unilateral hypertrophy ofthe lamina and spinous process of C5 vertebra coexistence with Klippel-Feil syndrome,occipitalization of atlas and atlantoaxial congenital fusion. Because of cosmetic anomalypatient underwent surgery and spinous process excised. To the best of our knowledge, thiscoexistence of congenital cervical bony anomalies in a child has not been reported previouslyin English literature.

Özet

Konjenital servikal omurga anomalileri sık olarak alt ve üst servikal bölgede görülebilir.Ancak, tek taraflı lamina ve spinöz proçes hipertrofisi oldukça nadirdir. Literatür taramamızdayayınlamış sadece 4 vaka bulabildik. Burada, 11 yaşındaki bir kız çocuğunda estetikanormalliğe neden olan C5 vertebrasının tek taraflı spinöz proçes ve lamina hipertrofisiraporlanmıştır. Bu duruma ek olarak, Klippel-Feil Sendromu, atlasın oksipitalizasyonu veatlantoaksiyal konjenital füzyon eşlik etmektedir.Hasta kozmetik problemi nedeniyle opereedildi. Bilgilerimize göre, bu konjenital servikal anomalilerin birlikteliği daha önce bir kızçocuğunda bildirilmemiştir.

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Cite This Article

UMUR, A. Ş., METE, M., SELÇUKİ, M., DURANSOY, Y. K., ÜNSAL, Ü. Ü. (2022). Klippel-Feil Sendromunda C5 Spinöz Proçesinin Dev Hipertrofisi. Journal of Neurological Sciences (Turkish), Cilt: 32 - Sayı: 3, 575–579. https://ajindex.com/articles/564910

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