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Journals / Journal of Istanbul University Faculty of Dentistry / 2017 / Cilt: 51 - Sayı: 2

Marfan Sendromunda Dental Bulgular: Olgu Sunumu

DENTAL FINDINGS IN MARFAN SYNDROME: A CASE REPORT

Nimet ÜNLÜ
Büşra BOSTANCI
Emre KORKUT
Pages
61–67
Publication Date
2022-10-18
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

The patient was advised to visit regularly for follow up and she was referred for orthodontic evaluation

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Marfan syndrome is an autosomal dominant disorder of connective tissue primarily characterized with anomalies affecting the musculoskeletal system, the cardiovascular system and the eyes.
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Key Findings & Data:A 7-year-old female was referred to our clinic, with a chief complaint of dental crowding in the anterior region of mandible.
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Conclusion & Impact:The patient was advised to visit regularly for follow up and she was referred for orthodontic evaluation
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Marfan syndrome is an autosomal dominant disorder of connective tissue primarily characterized with anomalies affecting the musculoskeletal system, the cardiovascular system and the eyes. It has been suggested that early diagnosis of the syndrome is important, because of the risk of infective endocarditis. A 7-year-old female was referred to our clinic, with a chief complaint of dental crowding in the anterior region of mandible. It was observed that the patient needed multiple treatments based on detailed clinical and radiographic examinations. The treatment was carried out with antibiotic prophylaxis an hour prior to her appointment considering her profound caries. The patient was advised to visit regularly for follow up and she was referred for orthodontic evaluation

Özet

Marfan sendromu, öncelikle kas-iskelet sistemi, kalp-damar sistemi ve gözleri etkileyen anomaliler ile karakterize, otozomal dominant bir bağ dokusu hastalığıdır. Enfektif endokardit riski nedeniyle sendromun erken tanısının önemli olduğu ileri sürülmektedir. 7 yaşındaki kadın hasta alt çenenin ön bölgesindeki dişlerin çapraşıklığı şikâyeti ile kliniğimize başvurdu. Ayrıntılı klinik ve radyografik muayene sonucu hastanın çoklu tedavi ihtiyacı olduğu belirlendi. Hastanın derin çürükleri dikkate tedaviler girişimden bir saat önce olacak şekilde tasarlanan antibiyotik proflaksisi altında gerçekleştirildi. Hastaya diş hekimine düzenli olarak gelmesi önerildi ve ortodontik değerlendirilmeye yönlendirildi

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Cite This Article

ÜNLÜ, N., BOSTANCI, B., KORKUT, E. (2022). Marfan Sendromunda Dental Bulgular: Olgu Sunumu. Journal of Istanbul University Faculty of Dentistry, Cilt: 51 - Sayı: 2, 61–67. https://ajindex.com/articles/563776

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