Journals / İstanbul Kuzey Klinikleri / 2018 / Cilt: 5 - Sayı: 3

Evaluation of childhood solid pseudopapillary tumors of the pancreas

Pages
207–210
Publication Date
2022-10-18
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

The survival rate is quite high after radical resection.

📌 3 Key Takeaways

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Objective & Hypothesis:OBJECTIVE: Solid pseudopapillary tumor (SPT) of the pancreas is an extremely rare primary tumor in the pediatric agegroup.
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Key Findings & Data:Local recurrence and distant metastasis has only rarely been reported following incomplete resection.METHODS: A retrospective review of the medical records of 6 patients diagnosed as SPT according to a histopathologicalexamination at the Children’s Hospital of Erciyes University School of Medicine between 2010 and 2017 was performed.Demographic characteristics, tumor localization and size, diagnostic method, immunohistochemical staining features, andmedical and surgical treatments employed were recorded.RESULTS: There were 4 girls and 2 boys with the diagnosis of SPT included in this study.
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Conclusion & Impact:The survival rate is quite high after radical resection.
🔬Design:Review & Systematic Survey
📍Scope:2010 Verileri
⚙️Variables:Domain Parameters

Abstract

OBJECTIVE: Solid pseudopapillary tumor (SPT) of the pancreas is an extremely rare primary tumor in the pediatric agegroup. It has a low malignant potential and the prognosis is good if radical resection of the tumor is performed. Local recurrence and distant metastasis has only rarely been reported following incomplete resection.METHODS: A retrospective review of the medical records of 6 patients diagnosed as SPT according to a histopathologicalexamination at the Children’s Hospital of Erciyes University School of Medicine between 2010 and 2017 was performed.Demographic characteristics, tumor localization and size, diagnostic method, immunohistochemical staining features, andmedical and surgical treatments employed were recorded.RESULTS: There were 4 girls and 2 boys with the diagnosis of SPT included in this study. The mean age of the patients was14 years (min-max: 13–16 years). The most common presenting complaint was abdominal pain. The mass lesion was at thehead of the pancreas in 3 cases (50%) and the tail of the pancreas in the remaining 3 patients (50%). A Whipple procedure was performed in 3 cases, a distal pancreatectomy in 1, a distal pancreatectomy plus splenectomy in 1, and a subtotalpancreatectomy in 1patient. Immunohistochemistry revealed positive staining for beta-catenin, keratin, CD56, vimentin, andCD10 in all cases.CONCLUSION: SPT is a rarely seen pancreatic mass with low rate of malignancy. Diagnosis may be delayed due to itsasymptomatic nature in most cases and a lack of descriptive symptoms. The survival rate is quite high after radical resection.

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Cite This Article

ÖZCAN, A., PATIROĞLU, T., ÜNAL, E., ÖZDEMİR, M. A., ARSLANOĞLU, C., ÖZCAN, S. S., KARAKUKÇU, M., DENİZ, K. (2022). Evaluation of childhood solid pseudopapillary tumors of the pancreas. İstanbul Kuzey Klinikleri, Cilt: 5 - Sayı: 3, 207–210. https://ajindex.com/articles/551512

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