Eosinophilic fasciitis (shulman syndrome)

It is usually seen in young males, rarely inelderly women and in children.In this paper, we present a 45-year-old femalepatient who presented with complaints of painand tightness of the skin in the upper extremities.She was diagnosed as EF with the characteristicclinical features and histopathological findingsand responded well to systemic steroid therapy.

📌 3 Key Takeaways

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Objective & Hypothesis:Eosinophilic fasciitis (EF) is a rare inflammatorydisease of unknown etiology.

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Key Findings & Data:The characteristicfeatures of this inflammatory disease includescleroderma-like skin indurations, predominantly on the extremities, and peripheral blood eosinophilia.

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Conclusion & Impact:It is usually seen in young males, rarely inelderly women and in children.In this paper, we present a 45-year-old femalepatient who presented with complaints of painand tightness of the skin in the upper extremities.She was diagnosed as EF with the characteristicclinical features and histopathological findingsand responded well to systemic steroid therapy.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Eosinophilic fasciitis (EF) is a rare inflammatorydisease of unknown etiology. The characteristicfeatures of this inflammatory disease includescleroderma-like skin indurations, predominantly on the extremities, and peripheral blood eosinophilia. It is usually seen in young males, rarely inelderly women and in children.In this paper, we present a 45-year-old femalepatient who presented with complaints of painand tightness of the skin in the upper extremities.She was diagnosed as EF with the characteristicclinical features and histopathological findingsand responded well to systemic steroid therapy.

Özet

Eozinofilik fasit (EF) nadir görülen ve etiyolojisitam olarak bilinmeyen inflamatuvar bir hastalıktır.Periferal kanda eozinofili ve özellikle ekstremitelerde skleroderma benzeri deri endurasyonlarıbu hastalığın karakteristik özellikleridir. Genellikle genç erkeklerde, nadiren yaşlı kadınlarda veçocuklarda görülür.Bu yazıda üst ekstremitelerinde ağrı ve sertlik şikayetleri ile başvuran, karakteristik klinik özellikleri ve histopatolojik bulguları ile EF tanısı konulan ve sistemik steroid tedavisine iyi yanıt veren45 yaşındaki kadın olgu sunulmuştur.

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Cite This Article

ÇÖLGEÇEN, E., ERDOĞAN, Y., GÜNAYDIN, İ., YILDIRIM, N. E., KORKMAZ, M., ŞENARSLAN, D. A., OKUR, A. (2022). Eosinophilic fasciitis (shulman syndrome). Haydarpaşa Numune Eğitim ve Araştırma Hastanesi Tıp Dergisi, Cilt: 53 - Sayı: 2, 121–123. https://ajindex.com/articles/535385

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