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Journals / Erciyes Tıp Dergisi / 2007 / Cilt: 29 - Sayı: 3

Hereditary hemorrhagic telangiectasia with epistaxis: a case report

Herediter hemorajik telenjektazi: epistaksis nedeniyle bir olgu sunumu

Mahmut ÖZKIRIŞ
Pages
239–241
Publication Date
2022-10-17
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case report, in addition to anemia, a case whose lesions are evident in nasal mucosa is presented.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Hereditary hemorrhagic telangiectasia, Osler-Weber-Rendu, is a rare vascular disease in which telangiectasia, arteriovenous malformation, and aneurysm might be commonly found in the body.
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Key Findings & Data:The earliest symptom of the disease is usually epistaxis, which usually starts in the second pace.
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Conclusion & Impact:In this case report, in addition to anemia, a case whose lesions are evident in nasal mucosa is presented.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Hereditary hemorrhagic telangiectasia, Osler-Weber-Rendu, is a rare vascular disease in which telangiectasia, arteriovenous malformation, and aneurysm might be commonly found in the body. The earliest symptom of the disease is usually epistaxis, which usually starts in the second pace. Epistaxis can also be so intense that may even lead to anemia. In this case report, in addition to anemia, a case whose lesions are evident in nasal mucosa is presented.

Özet

Herediter Hemorajik Telenjektazi (HHT), diğer ismiyle Osler-Weber-Rendu Hastalığı, nadir görülen yaygın bir damar hastalığıdır. Telenjektazi, arteriovenöz malformasyon ve anevrizmalar vücutta yaygın olarak bulunabilir. Hastalığın en erken belirtisi genellikle ikinci dekatta başlayan epistaksistir. Epistaksis anemiye neden olabilecek kadar şiddetli olabilir. Makalemizde anemi ile birlikte burun mukozasında lezyonları belirgin olan bir olgu sunulmaktadır.

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Cite This Article

ÖZKIRIŞ, M. (2022). Hereditary hemorrhagic telangiectasia with epistaxis: a case report. Erciyes Tıp Dergisi, Cilt: 29 - Sayı: 3, 239–241. https://ajindex.com/articles/502737

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