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Journals / Eklem Hastalıkları ve Cerrahisi Dergisi (Eski Adı: Artroplasti Artroskopik Cerrahi Derg.) / 2011 / Cilt: 22 - Sayı: 1

Proteus sendromunun nadir görülen formu: Makrosindaktili

An unusual initial presentation of Proteus syndrome: macrosyndactyly

Cemil Yıldırım TÜRK
Mithat ÖNER
Mehmet HALICI
Ahmet GÜNEY
Pages
56–59
Publication Date
2022-10-18
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This article discusses the differential diagnosis of Proteus syndrome and the treatment methods used for macrodactyly along with the presentation of the case.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Proteus syndrome is a complex disorder characterized by a wide variety of deformities including macrodactyly.
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Key Findings & Data:In the present report, we present a case with complex macrosyndactyly in his hand.
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Conclusion & Impact:This article discusses the differential diagnosis of Proteus syndrome and the treatment methods used for macrodactyly along with the presentation of the case.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Proteus syndrome is a complex disorder characterized by a wide variety of deformities including macrodactyly. In the present report, we present a case with complex macrosyndactyly in his hand. The patient was surgically treated. However, he admitted with lymphangiomas on his body during the follow- up period, leading to the diagnosis of Proteus syndrome. This article discusses the differential diagnosis of Proteus syndrome and the treatment methods used for macrodactyly along with the presentation of the case.

Özet

Proteus sendromu makrodaktilinin de içinde bulunduğu çok çeşitli deformitelerle karakterize kompleks bir hastalıktır. Bu yazıda elinde kompleks makrosindaktili bulunan bir olgu sunuldu. Hasta cerrahi olarak tedavi edildi. Ancak daha sonraki takip döneminde vücudundaki lenfanjiyomlar ile başvurdu ve bu bulgu ile Proteus sendromu tanısı konuldu. Bu yazıda, olgu sunumuyla birlikte Proteus sendromunun ayırıcı tanısı ve makrosindaktilide uygulanan tedavi yöntemleri tartışıldı.

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Cite This Article

TÜRK, C. Y., ÖNER, M., HALICI, M., GÜNEY, A. (2022). Proteus sendromunun nadir görülen formu: Makrosindaktili. Eklem Hastalıkları ve Cerrahisi Dergisi (Eski Adı: Artroplasti Artroskopik Cerrahi Derg.), Cilt: 22 - Sayı: 1, 56–59. https://ajindex.com/articles/498672

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References (10)

  1. Wiedemann HR, Burgio GR, Aldenhoff P, Kunze J, Kaufmann HJ, Schirg E. The proteus syndrome. Partial gigantism of the hands and/or feet, nevi, hemihypertrophy, subcutaneous tumors, macrocephaly or other skull anomalies and possible accelerated growth and visceral affections. Eur J Pediatr 1983;140:5-12
  2. Barmakian JT, Posner MA, Silver L, Lehman W, Vine DT. Proteus syndrome. J Hand Surg Am 1992;17:32-4
  3. Miura H, Uchida Y, Ihara K, Sugioka Y. Macrodactyly in Proteus syndrome. J Hand Surg Br 1993;18:308-9
  4. Barsky AJ. Macrodactyly. J Bone Joint Surg [Am] 1967;49:1255-66
  5. Demetriades D, Hager J, Nikolaides N, Malamitsi-Puchner A, Bartsocas CS. Proteus syndrome: musculoskeletal manifestations and management: a report of two cases. J Pediatr Ort hop 1992;12:106 -13
  6. Guidera KJ, Brinker MR, Kousseff BG, Helal AA, Pugh LI, Ganey TM, et al. Overgrowth management in Klippel-Trenaunay-Weber and Proteus syndromes. J Pediatr Orthop 1993;13:459-66
  7. D’Costa H, Hunter JD, O’Sullivan G, O’Keefe D, Jenkins JP, Hughes PM. Magnetic resonance imaging in macromelia and macrodactyly. Br J Radiol 1996;69:502-7
  8. Ishida O, Ikuta Y. Long-term results of surgical treat-ment for macrodactyly of the hand. Plast Reconstr Surg 1998;102:1586 -90
  9. Tsuge K. Treatment of macrodactyly. J Hand Surg Am 1985;10:968-9
  10. Kalen V, Burwell DS, Omer GE. Macrodactyly of the hands and feet. J Pediatr Orthop 1988;8:311-5.