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Journals / Atatürk Üniversitesi Diş Hekimliği Fakültesi Dergisi / 2007 / Cilt: 17 - Sayı: 3

Osteogenesis imperfecta: A case report

Osteogenezis imperfekta: Bir olgu sunumu

Taşkın GÜRBÜZ
Mehmet Selçuk ÖZBEK
Elvan ÖZBEK
Pages
48–51
Publication Date
2022-10-10
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

The extreme bone fragility seen in patients suffering from osteogenesis imperfecta pose a series of problems with regard to behavior management and rendering of quality dental treatment.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Osteogenesis imperfecta, or brittle bone disease, is a heritable disorder characterized by increased bone fragility.
📊
Key Findings & Data:This article reports the case of a 7 year old child diagnosed with type I osteogenesis imperfecta, assessing the clinical features observed, with emphasis on the histological, oral and dental findings.
💡
Conclusion & Impact:The extreme bone fragility seen in patients suffering from osteogenesis imperfecta pose a series of problems with regard to behavior management and rendering of quality dental treatment.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Osteogenesis imperfecta, or brittle bone disease, is a heritable disorder characterized by increased bone fragility. This article reports the case of a 7 year old child diagnosed with type I osteogenesis imperfecta, assessing the clinical features observed, with emphasis on the histological, oral and dental findings. The histological examination of dentin often reveals presence of irregular dentinal tubules, amorphous areas and poor calcification. All caries teeth treated with stainless steel crowns. The extreme bone fragility seen in patients suffering from osteogenesis imperfecta pose a series of problems with regard to behavior management and rendering of quality dental treatment.

Özet

Osteogenezis imperfekta veya kırılgan kemik hastalığı, kemik kırılganlığında artış ile karakterize kalıtımsal bir bozukluktur. Bu olgu raporunda tip I tanısı konan 7 yaşında bir çocuğun diş, ağız ve histolojik bulguları vurgulanmıştır ve klinik özellikleri değerlendirilmiştir. Dentinin histolojik incelenmesinde, zayıf kalsifiye olmuş, şekilsiz alanlar ve düzensiz dentin tubulleri gözlemlenmiştir. Çürük dişler, paslanmaz çelik kuronlar kullanılarak restore edilmiştir. Bu hastalar, şiddetli kemik kırılmalarından zarar gördüklerinden dolayı, nitelikli diş tedavilerini sağlamak ve davranış yönetimi hususunda bir dizi sorunlar üzerinde durmak gereklidir.

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Cite This Article

GÜRBÜZ, T., ÖZBEK, M. S., ÖZBEK, E. (2022). Osteogenesis imperfecta: A case report. Atatürk Üniversitesi Diş Hekimliği Fakültesi Dergisi, Cilt: 17 - Sayı: 3, 48–51. https://ajindex.com/articles/452723

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