The patient underwent a successful surgicaltreatment of all pathologies at a single session.
📌 3 Key Takeaways
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Objective & Hypothesis:Scimitar syndrome is a rare congenital cardiac anomaly,which is characterized by anomalous right pulmonaryvenous return to the inferior vena cava.
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Key Findings & Data:In this article, wereport a six-month-old girl with the diagnosis of Scimitarsyndrome associated with ventricular septal defect,left pulmonary venous stenosis and severe pulmonaryhypertension.
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Conclusion & Impact:The patient underwent a successful surgicaltreatment of all pathologies at a single session.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Scimitar syndrome is a rare congenital cardiac anomaly,which is characterized by anomalous right pulmonaryvenous return to the inferior vena cava. In this article, wereport a six-month-old girl with the diagnosis of Scimitarsyndrome associated with ventricular septal defect,left pulmonary venous stenosis and severe pulmonaryhypertension. The patient underwent a successful surgicaltreatment of all pathologies at a single session.
Özet
Scimitar sendromu, anomalili sağ pulmoner venözdönüşün inferior vena kavaya olduğu, nadir görülen doğuştan bir kalp anomalisidir. Bu yazıda, ventrikülerseptal defekt sol pulmoner ven stenozu ve ciddi pulmoner hipertansiyon ile ilişkili Scimitar sendromu tanısı olan altı aylık bir kız olgu sunuldu. Hasta tüm patolojilerin tek seansta tedavi edildiği başarılı bir cerrrahitedavi geçirdi.
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Cite This Article
GÜZELMERİÇ, F., CEYRAN, H., BAŞARAN, M., KAFALI, E., ÇİNE, N., YILDIRIM, A., TUNCER, E., TÜZÜN, B. (2022). Ventriküler septal defekt ve sol pulmoner ven stenozu ile ilişkili Scimitar sendromu. Türk Göğüs Kalp Damar Cerrahisi Dergisi, Cilt: 21 - Sayı: 4, 1043–1045. https://ajindex.com/articles/424492
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