Polyarteritis nodosa in case of familial Mediterranean fever

Objective & Hypothesis:Familial Mediterranean fever (FMF) is an autosomal recessive diseasecharacterized by recurrent self-limited attacks of fever accompanied byperitonitis, pleuritis, and arthritis.

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Key Findings & Data:It is rarely observed in children, but its incidenceincreases in the presence of FMF.

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Conclusion & Impact:Physicians should be awareof this possible association.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Özet

Familial Mediterranean fever (FMF) is an autosomal recessive diseasecharacterized by recurrent self-limited attacks of fever accompanied byperitonitis, pleuritis, and arthritis. Protracted febrile myalgia syndrome(PFMS) is a rare form of vasculitic disease which is an uncommon dramaticmanifestation of FMF, characterized by severe crippling myalgia and highfever. Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis affectingmedium or small arteries. It is rarely observed in children, but its incidenceincreases in the presence of FMF. In this article we described a 14-year-oldchild diagnosed with FMF associated with PAN. Physicians should be awareof this possible association.

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Cite This Article

GÖKCE, İ., ALTUNTAŞ, Ü., FİLİNTE, D., ALPAY, H. (2018). Polyarteritis nodosa in case of familial Mediterranean fever. Turkish Journal of Pediatrics, Cilt: 60 - Sayı: 3, 326–330. https://ajindex.com/articles/412117

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