Çoklu omirilik tümörüyle birlikte seyreden nörofibromatosis-2 olgusu

Objective & Hypothesis:Neurofibromatosis -2 is rare in all neurocutaneos disorders.We report a case in a 20-year-old girl in whom magnetic resonance imaging revealed multiple supratentorial and infratentorial tumors associated with cervical extradural and thoracic intramedullary spinal schwannomas.

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Key Findings & Data:This combination is rarely seen.

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Conclusion & Impact:We conclude that there is a clinical entity of multiple spinal cord tumors associated with neurofibromatosis-2.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Neurofibromatosis -2 is rare in all neurocutaneos disorders.We report a case in a 20-year-old girl in whom magnetic resonance imaging revealed multiple supratentorial and infratentorial tumors associated with cervical extradural and thoracic intramedullary spinal schwannomas. This combination is rarely seen. We conclude that there is a clinical entity of multiple spinal cord tumors associated with neurofibromatosis-2.

Özet

Nörofibromatosis-2 az görülen bir nörokütanöz hastalıktır. Manyetik rezonans görüntülemede servikal ekstradural ve torakal omurilik içi schwannomlarla birlikte seyreden çok sayıda supratentoriyel ve intratentoriyel tümörü saptanan 20 yaşında bir kadın hasta sunuldu. Bu tümörlerin birlikte görülmesi nadirdir. Nörofibromatosis-2 ile birlikte olan çoklu omurilik tümörünün ayrı bir klinik durumu olduğu sonucuna vardık.

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Cite This Article

KOTİL, K., GÖZÜM, T., YILMAZ, C. (1998). Çoklu omirilik tümörüyle birlikte seyreden nörofibromatosis-2 olgusu. Turkish Neurosurgery, Cilt: 8 - Sayı: 1, 53–56. https://ajindex.com/articles/405243

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