The histopathological features of cerebellar hemangioblastoma: Two case reports

In this article, 2 cases of hemangioblastoma, diagnosed in our department of pathology are presented and the histopathological and the clinical features are discussed.

📌 3 Key Takeaways

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Objective & Hypothesis:Capillary hemangioblastomas are benign, highly vascular tumors of controversial origin limited almost exclusively to the central nervous system.

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Key Findings & Data:These tumors make up about 1 to 2 percent of all intracranial neoplasms and occur primarily in the posterior fossa.

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Conclusion & Impact:In this article, 2 cases of hemangioblastoma, diagnosed in our department of pathology are presented and the histopathological and the clinical features are discussed.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Hemanjiyoblastom · Hippel-Lindau hastalığı · Merkezi sinir sistemi hastalıkları

Abstract

Capillary hemangioblastomas are benign, highly vascular tumors of controversial origin limited almost exclusively to the central nervous system. These tumors make up about 1 to 2 percent of all intracranial neoplasms and occur primarily in the posterior fossa. Most commonly they develop in the cerebellum of male adults in the third through fifth decades of life. Although the majority of the cases arise sporadically, some hemangioblastomas are associated with the autosomal dominantly inherited disease, von Hippel-Lindau syndrome. In this article, 2 cases of hemangioblastoma, diagnosed in our department of pathology are presented and the histopathological and the clinical features are discussed.

Özet

Capillary hemangioblastomas are benign, highly vascular tumors of controversial origin limited almost exclusively to the central nervous system. These tumors make up about 1 to 2 percent of all intracranial neoplasms and occur primarily in the posterior fossa. Most commonly they develop in the cerebellum of male adults in the third through fifth decades of life. Although the majority of the cases arise sporadically, some hemangioblastomas are associated with the autosomal dominantly inherited disease, von Hippel-Lindau syndrome. In this article, 2 cases of hemangioblastoma, diagnosed in our department of pathology are presented and the histopathological and the clinical features are discussed.

Keywords

Hemanjiyoblastom Hippel-Lindau hastalığı Merkezi sinir sistemi hastalıkları Kraniyal fossa posterior Hemangioblastoma Hippel-Lindau Disease Central Nervous System Diseases Cranial Fossa Posterior

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Cite This Article

TUNA, E. B., GÜRAY, M., TOPAL, N., SADE, B., CANDA, M. Ş., ACAR, Ü. D., CANDA, T. (2000). The histopathological features of cerebellar hemangioblastoma: Two case reports. Turkish Journal of Cancer, Cilt: 30 - Sayı: 4, 167–174. https://ajindex.com/articles/368516

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