SavedAdd your journal

Journals / Anestezi Dergisi / 2000 / Cilt: 8 - Sayı: 2

Anesthetic management of spinal progressive muscle atrophy

Spinal progressif musküler atrofide anestezi uygulaması (Olgu sunumu)

İsmail KATI
Cengiz Bekir DEMİREL
Burhan KÖSEOĞLU
Ürfettin Abbasov HÜSEYİNOĞLU
Pages
126–128
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this study, anesthetic problems of a 5 months old infant with Werdnig-Hoffmann Disease (Spinal Progressive Muscle Atrophy) during bronchoscopy performed under general anesthesia for diffuse segmentary atelectasia in the left lung were discussed.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:In this study, anesthetic problems of a 5 months old infant with Werdnig-Hoffmann Disease (Spinal Progressive Muscle Atrophy) during bronchoscopy performed under general anesthesia for diffuse segmentary atelectasia in the left lung were discussed.
📊
Key Findings & Data:In this study, anesthetic problems of a 5 months old infant with Werdnig-Hoffmann Disease (Spinal Progressive Muscle Atrophy) during bronchoscopy performed under general anesthesia for diffuse segmentary atelectasia in the left lung were discussed.
💡
Conclusion & Impact:In this study, anesthetic problems of a 5 months old infant with Werdnig-Hoffmann Disease (Spinal Progressive Muscle Atrophy) during bronchoscopy performed under general anesthesia for diffuse segmentary atelectasia in the left lung were discussed.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Anestezi · Atelektazi · Çocukluk çağı spinal kas atrofisi

Abstract

In this study, anesthetic problems of a 5 months old infant with Werdnig-Hoffmann Disease (Spinal Progressive Muscle Atrophy) during bronchoscopy performed under general anesthesia for diffuse segmentary atelectasia in the left lung were discussed.

Özet

Bu çalışmada; Werdnig-Hoffmann Hastalığı (Spinal Progressif Musküler Atrofi) olan 5 aylık bir çocuğun sol akciğerindeki yaygın segmenter atelektazi nedeni ile yapılan bronkoskopi için uygulanan anestezide karşılaşılan sorunlar tartışılmıştır.

🔖

Cite This Article

KATI, İ., DEMİREL, C. B., KÖSEOĞLU, B., HÜSEYİNOĞLU, Ü. A. (2000). Anesthetic management of spinal progressive muscle atrophy. Anestezi Dergisi, Cilt: 8 - Sayı: 2, 126–128. https://ajindex.com/articles/355520

References (9)

  1. Duncan PG. Neuromuscular disease. In: Katz J, Steward DJ (eds) Anesthesia and Uncommon Pediatric Diseases, Philadelphia, W.B. Sounders Company 1993: 672-694
  2. Yamanouchi Y, Yamanouchi H, Becker LE. Synaptic alterations of anterior horn cells in Werdnig-Hoffmann disease. Pediatr Neurol 1996; 15: 32-5, 3. Burlet P, Burglen L, Clermont O, et al. Large scale deletions of the 5q 13 region are specific to Werdnig-Hoffmann disease, J Med Genet 1996; 33: 281-3
  3. Kutafîn IuF, Osipov SM, Osipov ES. Werdnig-Hoffmann's congenital spinal atrophy in nursing infants. Zh Nevropatol Psikhiatr İm S Korsakova 1991; 91: 15-8 (abst) 5. lannaccone ST, Browne RH, Samaha FJ, Buncher CR. Prospective study of spinal muscular atrophy before age 6 years. DCN/SMA Group. Pediatr Neurol 1993; 9: 187-93
  4. Ikemoto A, Hirona A, Matsumoto S, Akiguchi I, Kimura J. Synaptophysin expression in the anterior horn of Werdnig-Hoffmann disease. J Neurol Sci 1996; 136: 94-100 7. Shayevitz JR, Matteo RS. Decreased sensitivity to metacurine in the patients with upper motoneuron disease. Anesth Analg 1985; 64: 767-72
  5. Hogue CW, Itani MS, Martyn JA. Resistance to Dtubocurarine in lower motor neuron injury is related to increased acetylcholine receptor at the neuromuscular junction. Anesthesiology 1990; 73:703
  6. Azar I. The response of patients with neuromuscular disorder to muscle relaxants: A review. Anesthesiology 1984; 61: 173-4
  7. Shime N, Hosokawa T, Hori Y, Hashimoto T, Miyazaki M. Anesthetic management of a patient with progressive spinal muscular atrophy. Masui 1990; 39: 918-20
  8. Takeshita K, Sakai K, Satio A, Yoda K. Anesthetic management of spinal progressive muscle atrophy. Masui 1989; 38: 557-9
  9. Weston LA, Di Fazio CA. Labor analgesia and anesthesia in a patient with spinal muscular atrophy and vocal cord paralysis. A rare and unusual case report. Reg Anesth 1996; 21: 350-4.