Airway management in crouzon syndrome

Objective & Hypothesis:Crouzon syndrome is an autosomal dominant disorders in patients with craniosynostosis, hypertelorism, orbital proptosis, short upper lip, hypoplastic maxilla, relative prognathism and without extremity involvement.

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Key Findings & Data:We presented anaesthetic management of a Crouzon syndrome with craniosynostosis, abnormal cranial involvement, increased intracranial pressure, relative prognathism and without extremity involvement who undergoes ventriculo-peritoneal shunt operation.

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Conclusion & Impact:We wanted to emphasize the points which should be considered for patients with in providing anesthesia and airway patency in this syndrome.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Crouzon syndrome is an autosomal dominant disorders in patients with craniosynostosis, hypertelorism, orbital proptosis, short upper lip, hypoplastic maxilla, relative prognathism and without extremity involvement. We presented anaesthetic management of a Crouzon syndrome with craniosynostosis, abnormal cranial involvement, increased intracranial pressure, relative prognathism and without extremity involvement who undergoes ventriculo-peritoneal shunt operation. We wanted to emphasize the points which should be considered for patients with in providing anesthesia and airway patency in this syndrome.

Özet

Crouzon sendromu kranyosinostoz. hipertelorizm, orbital proptozis. küçük üst dudak, hipoplastik maksilla, relatif mandibuler prognotizm ve ekstremi t e gelişiminde gerilik ile karakter ize otozomal dominant geçen bir sendromdur. Kranyosinostozu, anormal kranium gelişimi, artmış kafa içi basıncı, rölatif mandibular prognotismi ve ekstremite gelişiminde geriliği olan Crouzon sendromlu bir olguyu sunduk. Bu sendronıda ventrikülo-peritoneal şant yerleştirilmesi ameliyatında anestezi yönetimi ve hava yolu yönetiminde dikkat edilmesi gereken noktaları vurgulamak istedik.

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Cite This Article

YILMAZLAR, A., NAZLI, B., OĞUZALP, H. (2012). Airway management in crouzon syndrome. Anestezi Dergisi, Cilt: 20 - Sayı: 3, 176–178. https://ajindex.com/articles/355210

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