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Journals / Dicle Tıp Dergisi / 2015 / Cilt: 42 - Sayı: 2

Akromegalinin nadir bir nedeni: McCune-Albright sendromu

A rare cause of acromegaly: McCune-Albright syndrome

Erdal BODAKÇİ
Mazhar Müslüm TUNA
FARUK KILINÇ
ZAFER PEKKOLAY
Hikmet SOYLU
ŞADİYE ALTUN TUZCU
Alpaslan Kemal TUZCU
Pages
242–244
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We report a case of acromegaly accom- panied with this syndrome.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:McCune-Albright syndrome is characterized by polyostat- ic fibrous dysplasia, brown spots on the skin (café au lait pigmentation) and autonomous endocrine hyperfunction.
📊
Key Findings & Data:Acromegaly is seen in 20% of patients.
💡
Conclusion & Impact:We report a case of acromegaly accom- panied with this syndrome.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

McCune-Albright syndrome is characterized by polyostat- ic fibrous dysplasia, brown spots on the skin (café au lait pigmentation) and autonomous endocrine hyperfunction. Early puberty and other endocrinological manifestations, such as acromegaly, gigantism and hypercortisolism are widely observed in the syndrome. Acromegaly is seen in 20% of patients. We report a case of acromegaly accom- panied with this syndrome.

Özet

McCune-Albright sendromu, poliostotik fibröz displazi, deride kahverenginde lekelenme (Cafe au lait lekeleri) ve otonomik endokrin hiperfonksiyon ile karakterize bir sendromdur. Bu sendromda yaygın olarak erken puberte ve diğer endokrinolojik manifestasyonlar örneğin akromegali, jigantizm, hiperkortizolizm görülebilir. Akromegali Mc-Cune-Albriht sendromlu hastaların % 20 sinde görülebilir. Biz bu sendroma eşlik eden bir akromegali vakasını sunduk

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Cite This Article

BODAKÇİ, E., TUNA, M. M., KILINÇ, F., PEKKOLAY, Z., SOYLU, H., TUZCU, Ş. A., TUZCU, A. K. (2015). Akromegalinin nadir bir nedeni: McCune-Albright sendromu. Dicle Tıp Dergisi, Cilt: 42 - Sayı: 2, 242–244. https://ajindex.com/articles/348868

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