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Journals / Türk Üroloji Dergisi/Turkish Journal of Urology / 2005 / Cilt: 31 - Sayı: 3

A rare anomaly of the kidney: Congenital megacalcosis: Report of two cases

Böbreğin nadir görülen bir anomalisi: Doğumsal megakalikozis: İki olgu sunumu

Yusuf KİBAR
Hidayet ÇOBAN
Fikret ERDEMİR
Gökhan KOMESLİ
Murat DAYANÇ
A. Fuat PEKER
Pages
444–447
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this study, we discussed the clinical features of two cases with megacalycosis with the relevant literature.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Introduction: Megacalycosis or Puigvert's disease is a rarely seen congenital anomaly of renal development characterized by caliceal dilatation, increased number of calyces, hypoplasia of the pyramids of Malpighi, and a normal renal pelvis.
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Key Findings & Data:Renal function is always normal and there is no evidence of obstruction to urinary flow.
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Conclusion & Impact:In this study, we discussed the clinical features of two cases with megacalycosis with the relevant literature.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Genişleme · patolojik · Böbrek

Abstract

Introduction: Megacalycosis or Puigvert's disease is a rarely seen congenital anomaly of renal development characterized by caliceal dilatation, increased number of calyces, hypoplasia of the pyramids of Malpighi, and a normal renal pelvis. Renal function is always normal and there is no evidence of obstruction to urinary flow. In the absence of complications, the disease is discovered incidentally in the course of urologic examination undertaken for a different reason. In this study, we discussed the clinical features of two cases with megacalycosis with the relevant literature.

Özet

Megakalikozis yada Puigvert hastalığı kalikslerde sayıca artış ve dilatasyonla karakterize, nadir görülen doğumsal böbrek anomalisi olup normal böbrek pelvisi ve Malpighi piramitlerinin hipoplazisi ile birliktedir. Böbrek fonksiyonları her zaman normaldir ve üriner akımda obstrüksiyona ait bulgu yoktur. İstenmeyen yan etkilerin yokluğunda bu hastalık farklı nedenlere bağlı yapılan üriner sistem incelemelerinde insidental olarak saptanmaktadır. Bu çalışmada doğumsal megakalikozis tanısı konulan 2 hastanın klinik özellikleri literatür eşliğinde tartışılmaktadır.

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Cite This Article

KİBAR, Y., ÇOBAN, H., ERDEMİR, F., KOMESLİ, G., DAYANÇ, M., PEKER, A. F. (2005). A rare anomaly of the kidney: Congenital megacalcosis: Report of two cases. Türk Üroloji Dergisi/Turkish Journal of Urology, Cilt: 31 - Sayı: 3, 444–447. https://ajindex.com/articles/328798

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