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Journals / Romatizma Dergisi / 2002 / Cilt: 17 - Sayı: 2

Rehabilitation outcomes in arthrogryposis multiplex congenita

Artrogripozis multipleks kongenitalı hastalarda rehabilitasyon sonuçları

Özbudak Sibel DEMİR
Z. Aydan KURTARAN
Füsun KÖSEOĞLU
Müfit AKYÜZ
Pages
83–87
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

At the end of the rehabilitation programme passive range of motion and ambulation degree increased.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Arthrogryposis Multiplex Congenita is a non progressive syndrome which is characterized by multiple joint contractures.
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Key Findings & Data:The average age of the patients (7 male, 3 female) was 5,72±3,43.
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Conclusion & Impact:At the end of the rehabilitation programme passive range of motion and ambulation degree increased.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Artrogripoz · Hastaneye yatırma · Doğumsal

Abstract

Arthrogryposis Multiplex Congenita is a non progressive syndrome which is characterized by multiple joint contractures. Its etiology has been unknown. Viral infections and autosomal dominant transitions have been blamed for it. The aim of the study was to evaluate clinic and demographic characteristics and to investigate the progress of joint limitations and ambulation ability during rehabilitation. Prenatal, natal, postnatal features and progresses of the patients involved in this study have been noted. The localication and degree of the joint contractures been identified. Their ambulation ability and treatment applied have been assessed. The average age of the patients (7 male, 3 female) was 5,72±3,43. The length of stay at the rehabilitation center was 72,23±0,22 days. Breech presentation in 6 (%60) of the patients was established. 4 (%40) of the patients had congenital hip dislocation and 3 (%30) of them had genital anomaly. The joints in which contracture were the most freguenty localized were knee (%90), ankle (%80) and hip (%70) joints. At the end of the rehabilitation programme passive range of motion and ambulation degree increased.

Özet

Artrogripozis Multipleks Kongenita (AMK) ekstremitelerde multiple eklem kontraktürleri ile karakterize nonprogresif konjenital bir sendromdur. Etyolojisi tam olarak bilinmemekte, viral enfeksiyonlar veya otozomal dominant geçiş sorumlu tutulmaktadır. Bu çalışmanın amacı AMK'lı hastaları klinik, demografik özellikler açısından değerlendirmek ve rehabilitasyon sürecinde eklem limitasyonları ve ambülasyon seviyesinde kaydedilen gelişmeleri ortaya koymaktır. Çalışma kapsamına alınan hastaların prenatal, natal, postnatal özellikleri, gelişim evreleri kaydedilerek klinik özellikleri, eklem kontraktürlerinin lokalizasyonu ve derecesi, yatış ve çıkış ambülasyon seviyeleri ile uygulanan tedaviler değerlendirildi. 7'si erkek 3'ü kız toplam 10 hastanın yaş ortalaması 5,72±3,43, rehabilitasyon süresi ortalaması 72,23±0,22 gün idi. 6 (%60) hastada makad geliş tespit edildi. 4(%40) hastada doğumsal kalça çıkığı, 3(%30) hastada genital anomali mevcuttu. Kontraktürün en sık lokalize olduğu eklemler diz (%90). ayak bileği (%80) ve kalça (%70) idi. Rehabilitasyon programı sonucunda pasif eklem hareket açıklıklarında ve ambulasyon seviyelerinde artış saptandı.

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Cite This Article

DEMİR, Ö. S., KURTARAN, Z. A., KÖSEOĞLU, F., AKYÜZ, M. (2002). Rehabilitation outcomes in arthrogryposis multiplex congenita. Romatizma Dergisi, Cilt: 17 - Sayı: 2, 83–87. https://ajindex.com/articles/306049

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