Important congenital anomalies associated with VACTERL association and prematurity are very serious causes of mortality in the early period
📌 3 Key Takeaways
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Objective & Hypothesis:We report on a preterm male (birth weight 1,100 g) with bilateral renal agenesis, a lethal malformation.
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Key Findings & Data:Additionally, the child suffered from an atrial septal defect, ventricular septal defect, right aortic arch anomaly, a high type of anal atresia, vertebral anomalies, limbs defects (VACTERL association).
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Conclusion & Impact:Important congenital anomalies associated with VACTERL association and prematurity are very serious causes of mortality in the early period
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
We report on a preterm male (birth weight 1,100 g) with bilateral renal agenesis, a lethal malformation. Additionally, the child suffered from an atrial septal defect, ventricular septal defect, right aortic arch anomaly, a high type of anal atresia, vertebral anomalies, limbs defects (VACTERL association). The infant during first day of life was treated with an emergency sigmoid ostomy and peritoneal dialysisbecause of increasing abdominal dilatation and high urea and creatinine levels in blood. Important congenital anomalies associated with VACTERL association and prematurity are very serious causes of mortality in the early period
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Cite This Article
BASUGUY, E., AKDENİZ, S., ERTUĞRUL, S. (2017). Bilateral renal agenesis, a severe anomaly in a premature infant with VACTERL association: A case report. Pediatric Urology Case Reports, Cilt: 4 - Sayı: 6, 387–390. https://ajindex.com/articles/285625
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