SavedAdd your journal

Journals / Medicine Science / 2019 / Cilt: 8 - Sayı: 3

Successful use of spinal anesthesia for incarcerated inguinal hernia repair in a patient with Hunter syndrome

Neslihan ALTUNKAYA
Duygu Demiroz ASLAN
Pages
754–755
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this report we present spinal anesthesia that was administered to a patient with Hunter syndrome to avoid complications related to anticipated difficult airway.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Mucopolysaccharidosis type II (MPS II, Hunter syndrome) is a rare X-linked lysosomal storage disorder caused by a deficiency of the enzyme iduronate-2-sulphatase, leading to the accumulation of glycosaminoglycan (GAG).
📊
Key Findings & Data:GAG accumulation causes difficult airway due to changes in the upper airway.
💡
Conclusion & Impact:In this report we present spinal anesthesia that was administered to a patient with Hunter syndrome to avoid complications related to anticipated difficult airway.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Özet

Mucopolysaccharidosis type II (MPS II, Hunter syndrome) is a rare X-linked lysosomal storage disorder caused by a deficiency of the enzyme iduronate-2-sulphatase, leading to the accumulation of glycosaminoglycan (GAG). GAG accumulation causes difficult airway due to changes in the upper airway. In this report we present spinal anesthesia that was administered to a patient with Hunter syndrome to avoid complications related to anticipated difficult airway.

🔖

Cite This Article

ALTUNKAYA, N., ASLAN, D. D. (2019). Successful use of spinal anesthesia for incarcerated inguinal hernia repair in a patient with Hunter syndrome. Medicine Science, Cilt: 8 - Sayı: 3, 754–755. https://ajindex.com/articles/277139

📄 Full Text PDF Viewer

📄

PDF görüntüleyici hazırlanıyor...

References (7)

  1. Neufeld EF, Muenzer J. The mucopolysaccharidoses. In: Scriver CR, Beaudet AL, Sly WS, Valle D, editors. The metabolic and molecular bases of inherited disease. New York: McGraw–Hill; 2001. p. 3421-52
  2. Kreidstein A, Boorin MR, Crespi J, et al. Delayed awakening from anaesthesia in a patient with Hunter syndrome, Can J Anaesth. 1994;41:423-6
  3. Young ID, Harper PS. Mild form of Hunter’s syndrome: clinical delineation based on 31 cases. Arch Dis Child. 1982;57:828-36
  4. Baum VC, O’Flaherty JE. Anesthesia for genetic, metabolic and dysmorphic syndromes of childhood. 1st edition. Philadelphia: Lippincot Williams and Wilkins; 1999.p. 144-5
  5. Frawley G, Fuenzalida D, Donath S, et al. A retrospective audit of anesthetic techniques and complications in children with mucopolysaccharidoses. Paediatr Anaesth. 2012;22:737-44 6. Özer AB, Beştaş A, Erhan ÖL, ve ark. Mukopolisakkaridozlu iki kardeşte anestezi uygulaması. Fırat Üniversitesi Dergisi. 2007:21:91-4
  6. Vas L. Preanaesthetic evaluation and premedication in Paediatrics. Indian J Anaesth. 2004;48:347-53
  7. Kumar KR, Kumar H, Baidya DK, et al. Successful use of spinal anesthesia for inguinal hernia repair in a child with Hunter syndrome with difficult airway J Clin Anesth. 2016;30:99-100.