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Journals / İzmir Dr. Behçet Uz Çocuk Hastanesi Dergisi / 2011 / Cilt: 1 - Sayı: 1

A case of Henoch Schönlein Purpura with serious multisystem involvement

Ciddi multisistemik tutulum ile seyreden Henoch Schönlein Purpura olgusu

Fatma KILIÇ KAYA
Özlem BAĞ İNCE
DEMET CAN
Serdar ALTINÖZ
Aysel ÖZTÜRK
Pages
33–36
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

During follow-up Familial Mediterranean Fever mutation positivity was also found.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Henoch Schönlein Purpura (HSP) is the most frequently seen pediatric vasculitis syndrome Although it has a benign nature, it may be seen with different system involvement and may have an atypical clinical presentation.
📊
Key Findings & Data:Here we present an atypical case of HSP with multi-system involvement not responding to corticosteroid treatment.
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Conclusion & Impact:During follow-up Familial Mediterranean Fever mutation positivity was also found.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Henoch Schönlein Purpura (HSP) is the most frequently seen pediatric vasculitis syndrome Although it has a benign nature, it may be seen with different system involvement and may have an atypical clinical presentation. Here we present an atypical case of HSP with multi-system involvement not responding to corticosteroid treatment. During follow-up Familial Mediterranean Fever mutation positivity was also found.

Özet

Henoch Schönlein Purpurası (HSP) çocukluk çağında en sık görülen vaskülitik sendromdur. Benign seyirli olmasına rağmen farklı sistem tutulumları ile karşımıza gelebilir, atipik klinik prezentasyon gösterebilir. Aşağıda multisistem tutulumu ve kortikosteroid tedavisine yanıt vermemesi nedeniyle atipik klinik seyir gösterdiği düşünülen ve izlemde FMF mutasyonu pozitif bulunan bir HSP olgusu sunulmuştur.

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Cite This Article

KAYA, F. K., İNCE, Ö. B., CAN, D., ALTINÖZ, S., ÖZTÜRK, A. (2011). A case of Henoch Schönlein Purpura with serious multisystem involvement. İzmir Dr. Behçet Uz Çocuk Hastanesi Dergisi, Cilt: 1 - Sayı: 1, 33–36. https://ajindex.com/articles/268720

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