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Journals / Gülhane Tıp Dergisi / 2005 / Cilt: 47 - Sayı: 2

Anesthetic management of microlaryngeal surgery in a patient with epidermolysis bullosa: A case report

Epidermolizis büllozalı hastada mikrolaringeal cerrahinin anestezi yönetimi: 0lgu sunumu

Zehra YANGIN
Kerem ERKALP
Hamdi DELATİOĞLU
A. Emre İLHAN
Numan KÖKTEN
Pages
150–152
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We report the succesful general anesthesia performed in a 16-year-old patient with epidermolysis bullosa with laryngeal webbing, and summary the main topics of the disease for anesthesiologists and otolaryngologists who care for these patients.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Epidermolysis bullosa is a hereditary disease characterized by bullae and crut-like lesions of the skin and mucosa that arise spontaneously or following trauma.
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Key Findings & Data:Because each manipulation on the skin and mucosa in these patients may cause formation of new lesions, anesthetic management of patients with epidermolysis butlosa should be directed towards as minimal monitoring and trauma as possible.
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Conclusion & Impact:We report the succesful general anesthesia performed in a 16-year-old patient with epidermolysis bullosa with laryngeal webbing, and summary the main topics of the disease for anesthesiologists and otolaryngologists who care for these patients.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Anestezi · genel · Ergen

Abstract

Epidermolysis bullosa is a hereditary disease characterized by bullae and crut-like lesions of the skin and mucosa that arise spontaneously or following trauma. Because each manipulation on the skin and mucosa in these patients may cause formation of new lesions, anesthetic management of patients with epidermolysis butlosa should be directed towards as minimal monitoring and trauma as possible. We report the succesful general anesthesia performed in a 16-year-old patient with epidermolysis bullosa with laryngeal webbing, and summary the main topics of the disease for anesthesiologists and otolaryngologists who care for these patients.

Özet

Epidermotizis bülloza (EB), mukozalarda ve ciltte kendiliğinden ya da travmatik olarak oluşan, bül ve krut benzeri lezyonlarta karakterize, genetik geçişli bir hastalıktır. Bu hastaların anestezi uygulamalarında, mukoza ve ciltteki her işlem, yeni lezyon oluşumuna neden olabileceği için, mümkün olan en az travma ve monitorizasyon uygulanmalıdır. Bu yazıda laringeal web'i olan 16 yaşındaki EB'lı olgudaki başarılı genel anestezi uygulaması ve bu hastalarla ilgilenen anestezi ve kulak burun boğaz hastalıktan hekimleri için hastalığın anahatları sunulmuştur.

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Cite This Article

YANGIN, Z., ERKALP, K., DELATİOĞLU, H., İLHAN, A. E., KÖKTEN, N. (2005). Anesthetic management of microlaryngeal surgery in a patient with epidermolysis bullosa: A case report. Gülhane Tıp Dergisi, Cilt: 47 - Sayı: 2, 150–152. https://ajindex.com/articles/226235

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