Association of Prune belly syndrome and horse shoe kidney (case report)

Objective & Hypothesis:A male fetus with a gestational age of 15 weeks with abdominal muscular and umbilical cord vessel anomalies in addition to urinary system anomalies is presented in this article.

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Key Findings & Data:The association of Prune belly syndrome characterized with urinary system anomalies and abdominal muscular hypoplasia/agenesis with multicystic renal dysplasia is well known.

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Conclusion & Impact:This case is presented because the association of horse shoe kidney with this syndrome has not been reported before.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Prune Belly sendromu · Anomaliler · çoklu

Abstract

A male fetus with a gestational age of 15 weeks with abdominal muscular and umbilical cord vessel anomalies in addition to urinary system anomalies is presented in this article. The association of Prune belly syndrome characterized with urinary system anomalies and abdominal muscular hypoplasia/agenesis with multicystic renal dysplasia is well known. This case is presented because the association of horse shoe kidney with this syndrome has not been reported before.

Özet

Bu makalede üriner sistem anomalilerinin yanı sıra abdominal kas ve umbilikal arter anomalisi olan 15 haftalık bir erkek fetus sunulmaktadır. Üriner sistem anomalileri ve abdominal kasların hipoplazisi/agenezisi ile karakterize Prune belly sendromunun multikistik renal displazi ile birlikteliği bilinmektedir. Olgu, bu sendrom ile at nalı böbrek birlikteliğinin bildirilmemiş olması nedeniyle sunulmaktadır

Keywords

Prune Belly sendromu Anomaliler çoklu Doğum öncesi tanı Düşük istemli Fetüs Prune Belly Syndrome Abnormalities Multiple Prenatal Diagnosis Abortion Induced Fetus

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Cite This Article

ÖZCAN, A., GÜNAL, A., ALÖMEROĞLU, M., CEYHAN, S. T., TUNCEL, Y., BAŞER, İ. (2008). Association of Prune belly syndrome and horse shoe kidney (case report). Gülhane Tıp Dergisi, Cilt: 50 - Sayı: 4, 276–278. https://ajindex.com/articles/226172

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