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Journals / Journal of Scientific Reports-A / 2007 / Issue: 014

A CASE WITH WOLFRAM (DIDMOAD) SYNDROME AND ORAL FINDINGS (A CASE REPORT)

WOLFRAM (DIDMOAD) SENDROMU BULUNAN BİR OLGUDAKİ ORAL BULGULAR (OLGU BİLDİRİMİ)

Hasan Hatipoğlu
Müjgan Güngör Hatipoğlu
Özden Kansu
Pages
137–140
Publication Date
2007-12-17
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Oral clinical and radiological findings were presented.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Wolfram Syndrome is an unusual, congenital, multi system disorder.
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Key Findings & Data:In this case report we present 20 year old-male patient, that was have Wolfram syndrome.
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Conclusion & Impact:Oral clinical and radiological findings were presented.
🔬Design:Araştırma Makalesi
📍Scope:Comprehensive Sample
⚙️Variables:Wolfram sendromu · DIDMOAD · oral bulgular

Abstract

Wolfram Syndrome is an unusual, congenital, multi system disorder. Diabetes mellitus, Diabetes insipidus, optic atrophy and deafness are most observable symptoms. Neurological, urinary tract and psychiatric disorders are the other common symptoms. Diabetes mellitus and optic atrophy are usually the first findings. In this case report we present 20 year old-male patient, that was have Wolfram syndrome. Oral clinical and radiological findings were presented.

Özet

Wolfram Sendromu, nadir görülen konjenital, birçok sistemi etkileyebilen sendromdur. Diabetes mellitus, diabetes insipidus, optik atrofi ve sağırlık ile karakterizedir. Hastalarda nörolojik rahatsızlıklar ile üriner sistem rahatsızlıkları ve psikolojik rahatsızlıklar da izlenir. Diabetes mellitus ve optik atrofi ilk ortaya çıkan bulgulardır. Bu olgu raporunda 20 yaşındaki Wolfram sendromlu erkek hastanın klinik ve radyografik ağız bulguları sunulmaktadır.

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Cite This Article

Hatipoğlu, H., Hatipoğlu, M. G., Kansu, Ö. (2007). A CASE WITH WOLFRAM (DIDMOAD) SYNDROME AND ORAL FINDINGS (A CASE REPORT). Journal of Scientific Reports-A, Issue: 014, 137–140. https://ajindex.com/articles/1512361

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