Journals / Türkiye Çocuk Hastalıkları Dergisi / 2026 / Cilt: 8 Sayı: 3

Anomalous Origin of the Right Pulmonary Artery from Ascending nomalous Origin of the Right Pulmonary Artery from Ascending Aorta Associated with Aortopulmonary Window and Interrupted orta Associated with Aortopulmonary Window and Interrupted Aortic Arch: Successful Surgical Correction with a Single 3 ortic Arch: Successful Surgical Correction with a Single 3D Patch

Çıkan Aortadan Anormal Kaynaklanan Sağ Pulmoner Arter, Aortopulmoner Pencere ve Kesintili Arkus Aorta Birlikteliği: Tek 3d Yama ile Başarılı Cerrahi Düzeltme

Abdullah Kocabaş(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Fırat Kardelen(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Gayaz Akçurin(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Şükrü Mercan(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Gökhan Arslan(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Halil Ertuğ(Akdeniz University, Faculty of Medicine, Department of Child Health and Diseases, Pediatric Cardiology, Antalya, Turkey)
Pages
146–148
Publication Date
2014-06-01
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare congenital heart defect and generally associated with other cardiac anomalies.
📊
Key Findings & Data:Patients with AORPA have high pulmonary fl ow results in congestive heart failure and unilateral pulmonary hypertension.
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Conclusion & Impact:Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch
🔬Design:Makale
📍Scope:Comprehensive Sample
⚙️Variables:Çıkan aortadan anormal kaynaklanan sağ pulmoner arter · Aortopulmoner pencere · Konjenital kalp hastalığı

Abstract

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare congenital heart defect and generally associated with other cardiac anomalies. Patients with AORPA have high pulmonary fl ow results in congestive heart failure and unilateral pulmonary hypertension. Thus, it is frequently a fatal malformation in the neonatal or early infancy periods if early surgical repair is not performed. Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch

Özet

Çıkan aortadan anormal kaynaklanan sağ pulmoner arter (ÇAAKPA) nadir görülen bir konjenital kalp defekti olup genellikle başka kalp anomalilerine eşlik eder. ÇAAKPA’lı hastalarda artmış pulmoner kan akımı sonucunda konjestif kalp yetmezliği ve tek taraflı pulmoner hipertansiyon gelişir. Bu nedenle cerrahi düzeltme yapılmayan hastalar genellikle yenidoğan ya da erken süt çocukluğu döneminde hayatını kaybederler. Bu yazıda, ÇAAKPA, aortopulmoner pencere ve kesintili arkus aorta birlikteliği saptanan ve tek 3D ksenograft yama kullanılarak başarılı bir şekilde opere edilen 1.5 aylık kız hasta sunulmaktadır.

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Cite This Article

Kocabaş, A., Kardelen, F., Akçurin, G., Mercan, Ş., Arslan, G., Ertuğ, H. (2014). Anomalous Origin of the Right Pulmonary Artery from Ascending nomalous Origin of the Right Pulmonary Artery from Ascending Aorta Associated with Aortopulmonary Window and Interrupted orta Associated with Aortopulmonary Window and Interrupted Aortic Arch: Successful Surgical Correction with a Single 3 ortic Arch: Successful Surgical Correction with a Single 3D Patch. Türkiye Çocuk Hastalıkları Dergisi, Cilt: 8 Sayı: 3, 146–148. https://ajindex.com/articles/1435891

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